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Benign exophthalmos syndrome

MedGen UID:
930337
•Concept ID:
C4304668
•
Disease or Syndrome
Synonyms: benign exophthalmos syndrome; bes
SNOMED CT: Benign exophthalmos syndrome (719519007)
 
Monarch Initiative: MONDO:0019103

Definition

Benign exophthalmos syndrome is characterized by slowly progressive unilateral exophthalmos and ipsilateral mucosal turbinate hypertrophy, without intraorbital or intranasal lesions. [from MONDO]

Professional guidelines

PubMed

Thyroid nodules in Graves' disease: classification, characterization, and response to treatment.
Carnell NE, Valente WA
Thyroid 1998 Aug;8(8):647-52. doi: 10.1089/thy.1998.8.647. PMID: 9737358
Thyroid nodules in Graves' disease: classification, characterization, and response to treatment.
Carnell NE, Valente WA
Thyroid 1998 Jul;8(7):571-6. doi: 10.1089/thy.1998.8.571. PMID: 9709909
Thyroidectomy in patients with marked thyroid enlargement: airway management, morbidity, and outcome.
McHenry CR, Piotrowski JJ
Am Surg 1994 Aug;60(8):586-91. PMID: 8030813

Recent clinical studies

Etiology

Surgery for Thyroid Disease in Children.
Bruch SW
Adv Pediatr 2023 Aug;70(1):123-130. Epub 2023 May 26 doi: 10.1016/j.yapd.2023.04.005. PMID: 37422290
Paediatric thyroidectomy: When and why? A 25-year institutional experience.
Yeung F, Wong KP, Lang BH, Chung PH, Wong KK
J Pediatr Surg 2022 Jul;57(7):1196-1200. Epub 2022 Mar 13 doi: 10.1016/j.jpedsurg.2022.02.026. PMID: 35379490
Recurrent Intracranial Hypertension in a Toddler with Graves' Disease.
Vuijk FA, de Bruin C, Peeters-Scholte CMPCD, Notting IC
Horm Res Paediatr 2022;95(1):88-92. Epub 2022 Feb 15 doi: 10.1159/000522619. PMID: 35168232
W(h)ither orbital pseudotumor?
Agir H, Aburn N, Davis C, MacKinnon C, Tan ST
J Craniofac Surg 2007 Sep;18(5):1148-53. doi: 10.1097/scs.0b013e31814510bb. PMID: 17912101
Unilateral exophthalmos associated with ipsilateral mucosal turbinate hypertrophy: benign exophthalmos syndrome (BES). A description of a new clinical condition.
Bonavolontà G, Iuliano A, Bonavolontà P, Strianese D
Eur J Ophthalmol 2005 Nov-Dec;15(6):800-3. doi: 10.1177/112067210501500623. PMID: 16329069

Diagnosis

Surgery for Thyroid Disease in Children.
Bruch SW
Adv Pediatr 2023 Aug;70(1):123-130. Epub 2023 May 26 doi: 10.1016/j.yapd.2023.04.005. PMID: 37422290
Multiple cavernous hemangiomas in the orbit: A case report and review of the literature.
Deng C, Hu W
Medicine (Baltimore) 2020 Jul 17;99(29):e20670. doi: 10.1097/MD.0000000000020670. PMID: 32702816Free PMC Article
W(h)ither orbital pseudotumor?
Agir H, Aburn N, Davis C, MacKinnon C, Tan ST
J Craniofac Surg 2007 Sep;18(5):1148-53. doi: 10.1097/scs.0b013e31814510bb. PMID: 17912101
Orbital rhabdomyosarcoma in Noonan syndrome.
Jung A, Bechthold S, Pfluger T, Renner C, Ehrt O
J Pediatr Hematol Oncol 2003 Apr;25(4):330-2. doi: 10.1097/00043426-200304000-00014. PMID: 12679651
Hyperthyroidism.
Larsen PR
Dis Mon 1976 Jul;22(10):3-30. doi: 10.1016/s0011-5029(76)80004-1. PMID: 1047646

Therapy

Recurrent Intracranial Hypertension in a Toddler with Graves' Disease.
Vuijk FA, de Bruin C, Peeters-Scholte CMPCD, Notting IC
Horm Res Paediatr 2022;95(1):88-92. Epub 2022 Feb 15 doi: 10.1159/000522619. PMID: 35168232
Marine-Lenhart syndrome in a young girl.
Şen Y, Cimbek EA, Yuca SA, Gedik GK, Sarı O
J Pediatr Endocrinol Metab 2014 Jan;27(1-2):189-91. doi: 10.1515/jpem-2013-0302. PMID: 24057592
W(h)ither orbital pseudotumor?
Agir H, Aburn N, Davis C, MacKinnon C, Tan ST
J Craniofac Surg 2007 Sep;18(5):1148-53. doi: 10.1097/scs.0b013e31814510bb. PMID: 17912101
Orbital rhabdomyosarcoma in Noonan syndrome.
Jung A, Bechthold S, Pfluger T, Renner C, Ehrt O
J Pediatr Hematol Oncol 2003 Apr;25(4):330-2. doi: 10.1097/00043426-200304000-00014. PMID: 12679651
Hyperthyroidism.
Larsen PR
Dis Mon 1976 Jul;22(10):3-30. doi: 10.1016/s0011-5029(76)80004-1. PMID: 1047646

Prognosis

Less frequent requests for In-111 pentreotide and its brothers of endocrinological interest.
Cuccurullo V, Cascini GL, Tamburrini O, Mansi L, Rotondo A
Minerva Endocrinol 2011 Mar;36(1):41-52. PMID: 21460786
Thyroid nodules in Graves' disease: classification, characterization, and response to treatment.
Carnell NE, Valente WA
Thyroid 1998 Aug;8(8):647-52. doi: 10.1089/thy.1998.8.647. PMID: 9737358
Thyroid nodules in Graves' disease: classification, characterization, and response to treatment.
Carnell NE, Valente WA
Thyroid 1998 Jul;8(7):571-6. doi: 10.1089/thy.1998.8.571. PMID: 9709909
Thyroidectomy in patients with marked thyroid enlargement: airway management, morbidity, and outcome.
McHenry CR, Piotrowski JJ
Am Surg 1994 Aug;60(8):586-91. PMID: 8030813
Visual diagnosis of hematologic and oncologic diseases.
Blackburn P
Emerg Med Clin North Am 1993 May;11(2):273-335. PMID: 8491109

Clinical prediction guides

Less frequent requests for In-111 pentreotide and its brothers of endocrinological interest.
Cuccurullo V, Cascini GL, Tamburrini O, Mansi L, Rotondo A
Minerva Endocrinol 2011 Mar;36(1):41-52. PMID: 21460786
Genetic heterogeneity in familial nonmedullary thyroid carcinoma: exclusion of linkage to RET, MNG1, and TCO in 56 families. NMTC Consortium.
Lesueur F, Stark M, Tocco T, Ayadi H, Delisle MJ, Goldgar DE, Schlumberger M, Romeo G, Canzian F
J Clin Endocrinol Metab 1999 Jun;84(6):2157-62. doi: 10.1210/jcem.84.6.5798. PMID: 10372725
Thyroid nodules in Graves' disease: classification, characterization, and response to treatment.
Carnell NE, Valente WA
Thyroid 1998 Aug;8(8):647-52. doi: 10.1089/thy.1998.8.647. PMID: 9737358
Thyroid nodules in Graves' disease: classification, characterization, and response to treatment.
Carnell NE, Valente WA
Thyroid 1998 Jul;8(7):571-6. doi: 10.1089/thy.1998.8.571. PMID: 9709909
Thyroidectomy in patients with marked thyroid enlargement: airway management, morbidity, and outcome.
McHenry CR, Piotrowski JJ
Am Surg 1994 Aug;60(8):586-91. PMID: 8030813

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