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Typical Joubert syndrome MRI findings

MedGen UID:
832951
Concept ID:
CN228298
Finding

Professional guidelines

PubMed

Poretti A, Vitiello G, Hennekam RC, Arrigoni F, Bertini E, Borgatti R, Brancati F, D'Arrigo S, Faravelli F, Giordano L, Huisman TA, Iannicelli M, Kluger G, Kyllerman M, Landgren M, Lees MM, Pinelli L, Romaniello R, Scheer I, Schwarz CE, Spiegel R, Tibussek D, Valente EM, Boltshauser E
Orphanet J Rare Dis 2012 Jan 11;7:4. doi: 10.1186/1750-1172-7-4. PMID: 22236771Free PMC Article

Recent clinical studies

Etiology

Bukowy-Bieryllo Z, Rabiasz A, Dabrowski M, Pogorzelski A, Wojda A, Dmenska H, Grzela K, Sroczynski J, Witt M, Zietkiewicz E
J Med Genet 2019 Nov;56(11):769-777. Epub 2019 Jul 31 doi: 10.1136/jmedgenet-2018-105918. PMID: 31366608
Fehrenbach MK, Nestler U, Meixensberger J, Bernhard MK, Merkenschlager A, Weise S, Krause M
Childs Nerv Syst 2018 Jul;34(7):1423-1425. Epub 2018 Mar 5 doi: 10.1007/s00381-018-3767-0. PMID: 29508057
Musiime GM, Kinuthia DMW, Oyatsi DP, Manguyu W
BMC Res Notes 2017 Dec 6;10(1):696. doi: 10.1186/s13104-017-3033-7. PMID: 29208045Free PMC Article
Poretti A, Snow J, Summers AC, Tekes A, Huisman TAGM, Aygun N, Carson KA, Doherty D, Parisi MA, Toro C, Yildirimli D, Vemulapalli M, Mullikin JC; NISC Comparative Sequencing Program, Cullinane AR, Vilboux T, Gahl WA, Gunay-Aygun M
J Med Genet 2017 Aug;54(8):521-529. Epub 2017 Jan 13 doi: 10.1136/jmedgenet-2016-104425. PMID: 28087721
Khan AO, Oystreck DT, Seidahmed MZ, AlDrees A, Elmalik SA, Alorainy IA, Salih MA
Ophthalmology 2008 Dec;115(12):2286-9. doi: 10.1016/j.ophtha.2008.08.005. PMID: 19041481

Diagnosis

Zhu L, Xie L
Medicine (Baltimore) 2017 Dec;96(51):e8626. doi: 10.1097/MD.0000000000008626. PMID: 29390414Free PMC Article
Musiime GM, Kinuthia DMW, Oyatsi DP, Manguyu W
BMC Res Notes 2017 Dec 6;10(1):696. doi: 10.1186/s13104-017-3033-7. PMID: 29208045Free PMC Article
Bulgheroni S, D'Arrigo S, Signorini S, Briguglio M, Di Sabato ML, Casarano M, Mancini F, Romani M, Alfieri P, Battini R, Zoppello M, Tortorella G, Bertini E, Leuzzi V, Valente EM, Riva D
Am J Med Genet A 2016 Dec;170(12):3115-3124. Epub 2016 Aug 17 doi: 10.1002/ajmg.a.37938. PMID: 27530364
Lehman AM, Eydoux P, Doherty D, Glass IA, Chitayat D, Chung BY, Langlois S, Yong SL, Lowry RB, Hildebrandt F, Trnka P
Am J Med Genet A 2010 Jun;152A(6):1411-9. doi: 10.1002/ajmg.a.33416. PMID: 20503315Free PMC Article
Khan AO, Oystreck DT, Seidahmed MZ, AlDrees A, Elmalik SA, Alorainy IA, Salih MA
Ophthalmology 2008 Dec;115(12):2286-9. doi: 10.1016/j.ophtha.2008.08.005. PMID: 19041481

Therapy

Gunay-Aygun M, Parisi MA, Doherty D, Tuchman M, Tsilou E, Kleiner DE, Huizing M, Turkbey B, Choyke P, Guay-Woodford L, Heller T, Szymanska K, Johnson CA, Glass I, Gahl WA
J Pediatr 2009 Sep;155(3):386-92.e1. Epub 2009 Jun 21 doi: 10.1016/j.jpeds.2009.03.045. PMID: 19540516Free PMC Article

Prognosis

Fehrenbach MK, Nestler U, Meixensberger J, Bernhard MK, Merkenschlager A, Weise S, Krause M
Childs Nerv Syst 2018 Jul;34(7):1423-1425. Epub 2018 Mar 5 doi: 10.1007/s00381-018-3767-0. PMID: 29508057
Zhu L, Xie L
Medicine (Baltimore) 2017 Dec;96(51):e8626. doi: 10.1097/MD.0000000000008626. PMID: 29390414Free PMC Article
Musiime GM, Kinuthia DMW, Oyatsi DP, Manguyu W
BMC Res Notes 2017 Dec 6;10(1):696. doi: 10.1186/s13104-017-3033-7. PMID: 29208045Free PMC Article
Van De Weghe JC, Rusterholz TDS, Latour B, Grout ME, Aldinger KA, Shaheen R, Dempsey JC, Maddirevula S, Cheng YH, Phelps IG, Gesemann M, Goel H, Birk OS, Alanzi T, Rawashdeh R, Khan AO; University of Washington Center for Mendelian Genomics, Bamshad MJ, Nickerson DA, Neuhauss SCF, Dobyns WB, Alkuraya FS, Roepman R, Bachmann-Gagescu R, Doherty D
Am J Hum Genet 2017 Jul 6;101(1):23-36. Epub 2017 Jun 15 doi: 10.1016/j.ajhg.2017.05.010. PMID: 28625504Free PMC Article
Poretti A, Snow J, Summers AC, Tekes A, Huisman TAGM, Aygun N, Carson KA, Doherty D, Parisi MA, Toro C, Yildirimli D, Vemulapalli M, Mullikin JC; NISC Comparative Sequencing Program, Cullinane AR, Vilboux T, Gahl WA, Gunay-Aygun M
J Med Genet 2017 Aug;54(8):521-529. Epub 2017 Jan 13 doi: 10.1136/jmedgenet-2016-104425. PMID: 28087721

Clinical prediction guides

Zhu L, Xie L
Medicine (Baltimore) 2017 Dec;96(51):e8626. doi: 10.1097/MD.0000000000008626. PMID: 29390414Free PMC Article
Van De Weghe JC, Rusterholz TDS, Latour B, Grout ME, Aldinger KA, Shaheen R, Dempsey JC, Maddirevula S, Cheng YH, Phelps IG, Gesemann M, Goel H, Birk OS, Alanzi T, Rawashdeh R, Khan AO; University of Washington Center for Mendelian Genomics, Bamshad MJ, Nickerson DA, Neuhauss SCF, Dobyns WB, Alkuraya FS, Roepman R, Bachmann-Gagescu R, Doherty D
Am J Hum Genet 2017 Jul 6;101(1):23-36. Epub 2017 Jun 15 doi: 10.1016/j.ajhg.2017.05.010. PMID: 28625504Free PMC Article
Poretti A, Snow J, Summers AC, Tekes A, Huisman TAGM, Aygun N, Carson KA, Doherty D, Parisi MA, Toro C, Yildirimli D, Vemulapalli M, Mullikin JC; NISC Comparative Sequencing Program, Cullinane AR, Vilboux T, Gahl WA, Gunay-Aygun M
J Med Genet 2017 Aug;54(8):521-529. Epub 2017 Jan 13 doi: 10.1136/jmedgenet-2016-104425. PMID: 28087721
Lehman AM, Eydoux P, Doherty D, Glass IA, Chitayat D, Chung BY, Langlois S, Yong SL, Lowry RB, Hildebrandt F, Trnka P
Am J Med Genet A 2010 Jun;152A(6):1411-9. doi: 10.1002/ajmg.a.33416. PMID: 20503315Free PMC Article
Khan AO, Oystreck DT, Seidahmed MZ, AlDrees A, Elmalik SA, Alorainy IA, Salih MA
Ophthalmology 2008 Dec;115(12):2286-9. doi: 10.1016/j.ophtha.2008.08.005. PMID: 19041481

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