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Abnormal intrahepatic bile duct morphology

MedGen UID:
869157
•Concept ID:
C4023577
•
Anatomical Abnormality
Synonym: Abnormality of the intrahepatic bile duct
 
HPO: HP:0011040

Definition

An abnormality of the intrahepatic bile duct. [from HPO]

Professional guidelines

PubMed

Placental growth factor promotes tumour desmoplasia and treatment resistance in intrahepatic cholangiocarcinoma.
Aoki S, Inoue K, Klein S, Halvorsen S, Chen J, Matsui A, Nikmaneshi MR, Kitahara S, Hato T, Chen X, Kawakubo K, Nia HT, Chen I, Schanne DH, Mamessier E, Shigeta K, Kikuchi H, Ramjiawan RR, Schmidt TC, Iwasaki M, Yau T, Hong TS, Quaas A, Plum PS, Dima S, Popescu I, Bardeesy N, Munn LL, Borad MJ, Sassi S, Jain RK, Zhu AX, Duda DG
Gut 2022 Jan;71(1):185-193. Epub 2021 Jan 11 doi: 10.1136/gutjnl-2020-322493. PMID: 33431577Free PMC Article
Recent advances in the pathogenesis and management of biliary atresia.
Zagory JA, Nguyen MV, Wang KS
Curr Opin Pediatr 2015 Jun;27(3):389-94. doi: 10.1097/MOP.0000000000000214. PMID: 25944310Free PMC Article
Differential diagnosis of bile duct injury and ductopenia.
West AB, Chatila R
Semin Diagn Pathol 1998 Nov;15(4):270-84. PMID: 9845428

Recent clinical studies

Etiology

Proteome Landscapes of Human Hepatocellular Carcinoma and Intrahepatic Cholangiocarcinoma.
Yi X, Zhu J, Liu W, Peng L, Lu C, Sun P, Huang L, Nie X, Huang S, Guo T, Zhu Y
Mol Cell Proteomics 2023 Aug;22(8):100604. Epub 2023 Jun 22 doi: 10.1016/j.mcpro.2023.100604. PMID: 37353004Free PMC Article
Post-transplant cholangiopathy: Classification, pathogenesis, and preventive strategies.
de Vries Y, von Meijenfeldt FA, Porte RJ
Biochim Biophys Acta Mol Basis Dis 2018 Apr;1864(4 Pt B):1507-1515. Epub 2017 Jun 20 doi: 10.1016/j.bbadis.2017.06.013. PMID: 28645651
Imaging of choledochal cysts.
Lewis VA, Adam SZ, Nikolaidis P, Wood C, Wu JG, Yaghmai V, Miller FH
Abdom Imaging 2015 Aug;40(6):1567-80. doi: 10.1007/s00261-015-0381-4. PMID: 25682292
Congenital fibrocystic liver diseases.
Drenth JP, Chrispijn M, Bergmann C
Best Pract Res Clin Gastroenterol 2010 Oct;24(5):573-84. doi: 10.1016/j.bpg.2010.08.007. PMID: 20955960
Biliary atresia revisited.
Kahn E
Pediatr Dev Pathol 2004 Mar-Apr;7(2):109-24. Epub 2004 Mar 4 doi: 10.1007/s10024-003-0307-y. PMID: 14994122

Diagnosis

Portal biliopathy.
Khuroo MS, Rather AA, Khuroo NS, Khuroo MS
World J Gastroenterol 2016 Sep 21;22(35):7973-82. doi: 10.3748/wjg.v22.i35.7973. PMID: 27672292Free PMC Article
Imaging of choledochal cysts.
Lewis VA, Adam SZ, Nikolaidis P, Wood C, Wu JG, Yaghmai V, Miller FH
Abdom Imaging 2015 Aug;40(6):1567-80. doi: 10.1007/s00261-015-0381-4. PMID: 25682292
Molecular diagnosis of intrahepatic cholangiocarcinoma.
Haga H, Patel T
J Hepatobiliary Pancreat Sci 2015 Feb;22(2):114-23. Epub 2014 Sep 29 doi: 10.1002/jhbp.156. PMID: 25267595Free PMC Article
Biliary atresia.
Mieli-Vergani G, Vergani D
Semin Immunopathol 2009 Sep;31(3):371-81. Epub 2009 Jun 17 doi: 10.1007/s00281-009-0171-6. PMID: 19533128
Alagille syndrome.
Krantz ID, Piccoli DA, Spinner NB
J Med Genet 1997 Feb;34(2):152-7. doi: 10.1136/jmg.34.2.152. PMID: 9039994Free PMC Article

Therapy

Convergent MAPK pathway alterations mediate acquired resistance to FGFR inhibitors in FGFR2 fusion-positive cholangiocarcinoma.
DiPeri TP, Zhao M, Evans KW, Varadarajan K, Moss T, Scott S, Kahle MP, Byrnes CC, Chen H, Lee SS, Halim AB, Hirai H, Wacheck V, Kwong LN, Rodon J, Javle M, Meric-Bernstam F
J Hepatol 2024 Feb;80(2):322-334. Epub 2023 Nov 14 doi: 10.1016/j.jhep.2023.10.041. PMID: 37972659
Post-transplant cholangiopathy: Classification, pathogenesis, and preventive strategies.
de Vries Y, von Meijenfeldt FA, Porte RJ
Biochim Biophys Acta Mol Basis Dis 2018 Apr;1864(4 Pt B):1507-1515. Epub 2017 Jun 20 doi: 10.1016/j.bbadis.2017.06.013. PMID: 28645651
Portal biliopathy.
Khuroo MS, Rather AA, Khuroo NS, Khuroo MS
World J Gastroenterol 2016 Sep 21;22(35):7973-82. doi: 10.3748/wjg.v22.i35.7973. PMID: 27672292Free PMC Article
Diagnosis of IgG4-related sclerosing cholangitis.
Nakazawa T, Naitoh I, Hayashi K, Miyabe K, Simizu S, Joh T
World J Gastroenterol 2013 Nov 21;19(43):7661-70. doi: 10.3748/wjg.v19.i43.7661. PMID: 24282356Free PMC Article
Clinical characteristics of Caroli's syndrome.
Yonem O, Bayraktar Y
World J Gastroenterol 2007 Apr 7;13(13):1934-7. doi: 10.3748/wjg.v13.i13.1934. PMID: 17461493Free PMC Article

Prognosis

Circular RNAs in cholangiocarcinoma.
Liao W, Feng Q, Liu H, Du J, Chen X, Zeng Y
Cancer Lett 2023 Jan 28;553:215980. Epub 2022 Nov 4 doi: 10.1016/j.canlet.2022.215980. PMID: 36336149
Biliary atresia.
Mieli-Vergani G, Vergani D
Semin Immunopathol 2009 Sep;31(3):371-81. Epub 2009 Jun 17 doi: 10.1007/s00281-009-0171-6. PMID: 19533128
Clinical characteristics of Caroli's syndrome.
Yonem O, Bayraktar Y
World J Gastroenterol 2007 Apr 7;13(13):1934-7. doi: 10.3748/wjg.v13.i13.1934. PMID: 17461493Free PMC Article
Primary biliary cirrhosis.
Moreno-Otero R, Lisker-Melman M, Jones EA
Med Clin North Am 1989 Jul;73(4):911-29. doi: 10.1016/s0025-7125(16)30645-9. PMID: 2657267
Neonatal cholestasis.
Balistreri WF
J Pediatr 1985 Feb;106(2):171-84. doi: 10.1016/s0022-3476(85)80282-1. PMID: 3881579

Clinical prediction guides

Pemigatinib: A Review in Advanced Cholangiocarcinoma.
Frampton JE
Target Oncol 2024 Jan;19(1):107-114. Epub 2024 Jan 11 doi: 10.1007/s11523-023-01024-x. PMID: 38206555
Circular RNAs in cholangiocarcinoma.
Liao W, Feng Q, Liu H, Du J, Chen X, Zeng Y
Cancer Lett 2023 Jan 28;553:215980. Epub 2022 Nov 4 doi: 10.1016/j.canlet.2022.215980. PMID: 36336149
Diagnosis of IgG4-related sclerosing cholangitis.
Nakazawa T, Naitoh I, Hayashi K, Miyabe K, Simizu S, Joh T
World J Gastroenterol 2013 Nov 21;19(43):7661-70. doi: 10.3748/wjg.v19.i43.7661. PMID: 24282356Free PMC Article
Idiopathic adulthood ductopenia.
Nakano I, Fukuda Y, Koyama Y, Urano F, Yamada M, Katano Y, Marui A, Imada K, Hayakawa T, Ito M, Yamashita Y, Imoto M, Nakanuma Y
J Gastroenterol Hepatol 1996 Apr;11(4):411-5. doi: 10.1111/j.1440-1746.1996.tb01392.x. PMID: 8713711
Destructive intrahepatic bile duct diseases.
Desmet VJ
Recenti Prog Med 1990 Jun;81(6):392-8. PMID: 2251446

Recent systematic reviews

Association of mucin family members with prognostic significance in pancreatic cancer patients: A meta-analysis.
Xu W, Zhang M, Liu L, Yin M, Xu C, Weng Z
PLoS One 2022;17(6):e0269612. Epub 2022 Jun 16 doi: 10.1371/journal.pone.0269612. PMID: 35709153Free PMC Article
Risk of malignancy in Caroli disease and syndrome: A systematic review.
Fahrner R, Dennler SG, Inderbitzin D
World J Gastroenterol 2020 Aug 21;26(31):4718-4728. doi: 10.3748/wjg.v26.i31.4718. PMID: 32884228Free PMC Article
The role of imaging in determining prognosis for primary sclerosing cholangitis: A systematic review.
Segal D, Marotta P, Mosli M, Zou G, Feagan BG, Al-Judaibi B
Saudi J Gastroenterol 2019 May-Jun;25(3):152-158. doi: 10.4103/sjg.SJG_478_18. PMID: 31044745Free PMC Article
Meta-analysis of risk of developing malignancy in congenital choledochal malformation.
Ten Hove A, de Meijer VE, Hulscher JBF, de Kleine RHJ
Br J Surg 2018 Apr;105(5):482-490. Epub 2018 Feb 26 doi: 10.1002/bjs.10798. PMID: 29480528Free PMC Article
Therapeutic approaches for portal biliopathy: A systematic review.
Franceschet I, Zanetto A, Ferrarese A, Burra P, Senzolo M
World J Gastroenterol 2016 Dec 7;22(45):9909-9920. doi: 10.3748/wjg.v22.i45.9909. PMID: 28018098Free PMC Article

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