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Marfan syndrome, autosomal recessive

MedGen UID:
864496
Concept ID:
C4016059
Finding
Synonym: MARFAN SYNDROME, AUTOSOMAL RECESSIVE
 
OMIM®: 134797

Recent clinical studies

Etiology

van Bysterveldt KA, Al Taie R, Ikink W, Oliver VF, Vincent AL
Ophthalmic Genet 2017 Dec;38(6):537-543. Epub 2017 Apr 10 doi: 10.1080/13816810.2017.1309552. PMID: 28394649
Yang Y, Muzny DM, Xia F, Niu Z, Person R, Ding Y, Ward P, Braxton A, Wang M, Buhay C, Veeraraghavan N, Hawes A, Chiang T, Leduc M, Beuten J, Zhang J, He W, Scull J, Willis A, Landsverk M, Craigen WJ, Bekheirnia MR, Stray-Pedersen A, Liu P, Wen S, Alcaraz W, Cui H, Walkiewicz M, Reid J, Bainbridge M, Patel A, Boerwinkle E, Beaudet AL, Lupski JR, Plon SE, Gibbs RA, Eng CM
JAMA 2014 Nov 12;312(18):1870-9. doi: 10.1001/jama.2014.14601. PMID: 25326635Free PMC Article
Khan AO, Bolz HJ, Bergmann C
J AAPOS 2014 Apr;18(2):134-9. doi: 10.1016/j.jaapos.2013.11.012. PMID: 24698609
Le Goff C, Cormier-Daire V
Am J Med Genet C Semin Med Genet 2012 Aug 15;160C(3):145-53. Epub 2012 Jul 12 doi: 10.1002/ajmg.c.31337. PMID: 22791552
Lardeux A, Kyndt F, Lecointe S, Marec HL, Merot J, Schott JJ, Le Tourneau T, Probst V
J Cardiovasc Transl Res 2011 Dec;4(6):748-56. Epub 2011 Jul 20 doi: 10.1007/s12265-011-9308-9. PMID: 21773876

Diagnosis

Overwater E, Efrat R, Barge-Schaapveld DQCM, Lakeman P, Weiss MM, Maugeri A, van Tintelen JP, Houweling AC
Mol Genet Genomic Med 2019 Feb;7(2):e00518. Epub 2018 Nov 28 doi: 10.1002/mgg3.518. PMID: 30485715Free PMC Article
Yang Y, Muzny DM, Xia F, Niu Z, Person R, Ding Y, Ward P, Braxton A, Wang M, Buhay C, Veeraraghavan N, Hawes A, Chiang T, Leduc M, Beuten J, Zhang J, He W, Scull J, Willis A, Landsverk M, Craigen WJ, Bekheirnia MR, Stray-Pedersen A, Liu P, Wen S, Alcaraz W, Cui H, Walkiewicz M, Reid J, Bainbridge M, Patel A, Boerwinkle E, Beaudet AL, Lupski JR, Plon SE, Gibbs RA, Eng CM
JAMA 2014 Nov 12;312(18):1870-9. doi: 10.1001/jama.2014.14601. PMID: 25326635Free PMC Article
Ballabio E, Bersano A, Bresolin N, Candelise L
J Cereb Blood Flow Metab 2007 Oct;27(10):1649-62. Epub 2007 Jun 20 doi: 10.1038/sj.jcbfm.9600520. PMID: 17579657
Rumball KM, Pang E, Letts RM
J Pediatr Orthop B 1999 Apr;8(2):139-43. PMID: 10218180
Cacciari E, Salardi S
Haemostasis 1989;19 Suppl 1:10-3. doi: 10.1159/000216090. PMID: 2680808

Therapy

Sasai H, Shimozawa N, Asano T, Kawamoto N, Yamamoto T, Kimura T, Kawamoto M, Matsui E, Fukao T
Tohoku J Exp Med 2015 Dec;237(4):323-7. doi: 10.1620/tjem.237.323. PMID: 26639091
Rao TN, Radhakrishna K, Mohana Rao TS, Guruprasad P, Ahmed K
Indian J Dermatol Venereol Leprol 2008 Jul-Aug;74(4):375-8. doi: 10.4103/0378-6323.42916. PMID: 18797062
Naiglin L, Clayton J, Gazagne C, Dallongeville F, Malecaze F, Calvas P
Ann Genet 1999;42(3):140-6. PMID: 10526656
Coady MA, Davies RR, Roberts M, Goldstein LJ, Rogalski MJ, Rizzo JA, Hammond GL, Kopf GS, Elefteriades JA
Arch Surg 1999 Apr;134(4):361-7. doi: 10.1001/archsurg.134.4.361. PMID: 10199307

Prognosis

Morlino S, Alesi V, Calì F, Lepri FR, Secinaro A, Grammatico P, Novelli A, Drago F, Castori M, Baban A
Am J Med Genet A 2019 Jan;179(1):104-112. Epub 2018 Dec 18 doi: 10.1002/ajmg.a.10. PMID: 30565850
van Bysterveldt KA, Al Taie R, Ikink W, Oliver VF, Vincent AL
Ophthalmic Genet 2017 Dec;38(6):537-543. Epub 2017 Apr 10 doi: 10.1080/13816810.2017.1309552. PMID: 28394649
Kumar A, Duvvari MR, Prabhakaran VC, Shetty JS, Murthy GJ, Blanton SH
Hum Genet 2010 Oct;128(4):365-71. Epub 2010 Jul 9 doi: 10.1007/s00439-010-0858-8. PMID: 20617341
Rumball KM, Pang E, Letts RM
J Pediatr Orthop B 1999 Apr;8(2):139-43. PMID: 10218180
Maroteaux P, Frézal J, Cohen-Solal L
Am J Med Genet 1986 Jun;24(2):219-30. doi: 10.1002/ajmg.1320240203. PMID: 3717207

Clinical prediction guides

van Bysterveldt KA, Al Taie R, Ikink W, Oliver VF, Vincent AL
Ophthalmic Genet 2017 Dec;38(6):537-543. Epub 2017 Apr 10 doi: 10.1080/13816810.2017.1309552. PMID: 28394649
Yang Y, Muzny DM, Xia F, Niu Z, Person R, Ding Y, Ward P, Braxton A, Wang M, Buhay C, Veeraraghavan N, Hawes A, Chiang T, Leduc M, Beuten J, Zhang J, He W, Scull J, Willis A, Landsverk M, Craigen WJ, Bekheirnia MR, Stray-Pedersen A, Liu P, Wen S, Alcaraz W, Cui H, Walkiewicz M, Reid J, Bainbridge M, Patel A, Boerwinkle E, Beaudet AL, Lupski JR, Plon SE, Gibbs RA, Eng CM
JAMA 2014 Nov 12;312(18):1870-9. doi: 10.1001/jama.2014.14601. PMID: 25326635Free PMC Article
Le Goff C, Cormier-Daire V
Am J Med Genet C Semin Med Genet 2012 Aug 15;160C(3):145-53. Epub 2012 Jul 12 doi: 10.1002/ajmg.c.31337. PMID: 22791552
Azmanov DN, Dimitrova S, Florez L, Cherninkova S, Draganov D, Morar B, Saat R, Juan M, Arostegui JI, Ganguly S, Soodyall H, Chakrabarti S, Padh H, López-Nevot MA, Chernodrinska V, Anguelov B, Majumder P, Angelova L, Kaneva R, Mackey DA, Tournev I, Kalaydjieva L
Eur J Hum Genet 2011 Mar;19(3):326-33. Epub 2010 Nov 17 doi: 10.1038/ejhg.2010.181. PMID: 21081970Free PMC Article
Kumar A, Duvvari MR, Prabhakaran VC, Shetty JS, Murthy GJ, Blanton SH
Hum Genet 2010 Oct;128(4):365-71. Epub 2010 Jul 9 doi: 10.1007/s00439-010-0858-8. PMID: 20617341

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