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Progressive pulmonary failure

MedGen UID:
862009
•Concept ID:
C4013572
•
Disease or Syndrome

Professional guidelines

PubMed

Diagnosis and Treatment of Pulmonary Arterial Hypertension: A Review.
Ruopp NF, Cockrill BA
JAMA 2022 Apr 12;327(14):1379-1391. doi: 10.1001/jama.2022.4402. PMID: 35412560
Chronic obstructive pulmonary disease exacerbation fundamentals: Diagnosis, treatment, prevention and disease impact.
MacLeod M, Papi A, Contoli M, Beghé B, Celli BR, Wedzicha JA, Fabbri LM
Respirology 2021 Jun;26(6):532-551. Epub 2021 Apr 24 doi: 10.1111/resp.14041. PMID: 33893708
Pulmonary arterial hypertension: pathogenesis and clinical management.
Thenappan T, Ormiston ML, Ryan JJ, Archer SL
BMJ 2018 Mar 14;360:j5492. doi: 10.1136/bmj.j5492. PMID: 29540357Free PMC Article

Recent clinical studies

Etiology

Idiopathic pneumonia syndrome after high-dose chemotherapy and autologous hematopoietic stem cell transplantation for high-risk breast cancer.
Wong R, Rondon G, Saliba RM, Shannon VR, Giralt SA, Champlin RE, Ueno NT
Bone Marrow Transplant 2003 Jun;31(12):1157-63. doi: 10.1038/sj.bmt.1704141. PMID: 12796796
Diffuse alveolar hemorrhage in pediatric hematopoietic cell transplant patients.
Heggen J, West C, Olson E, Olson T, Teague G, Fortenberry J, Yeager AM
Pediatrics 2002 May;109(5):965-71. doi: 10.1542/peds.109.5.965. PMID: 11986464
Bronchiolitis obliterans organizing pneumonia (BOOP) in children after allogeneic bone marrow transplantation.
Mathew P, Bozeman P, Krance RA, Brenner MK, Heslop HE
Bone Marrow Transplant 1994 Feb;13(2):221-3. PMID: 8205095
Cranio-cervical decompression for Chiari I malformation. A retrospective evaluation of functional outcome with particular attention to the motor deficits.
Cristante L, Westphal M, Herrmann HD
Acta Neurochir (Wien) 1994;130(1-4):94-100. doi: 10.1007/BF01405508. PMID: 7725949
Determination of operability in candidates who undergo lung resection for bronchogenic carcinoma.
Murphy TP, Casey MT
Can J Surg 1990 Dec;33(6):470-3. PMID: 2253125

Diagnosis

A homozygous missense variant in the WRN gene segregating in a family with progressive pulmonary failure with recurrent spontaneous pneumothorax and interstitial lung disease.
Sezer A, Kayhan G, Gursoy TR, Eyuboglu TS, Percin FE
Am J Med Genet A 2023 Jan;191(1):220-227. Epub 2022 Oct 10 doi: 10.1002/ajmg.a.62986. PMID: 36214313
Lymphomatoid granulomatosis.
Roschewski M, Wilson WH
Cancer J 2012 Sep-Oct;18(5):469-74. doi: 10.1097/PPO.0b013e31826c5e19. PMID: 23006954
Reduction in mortality in pediatric patients with inhalation injury with aerosolized heparin/N-acetylcystine [correction of acetylcystine] therapy.
Desai MH, Mlcak R, Richardson J, Nichols R, Herndon DN
J Burn Care Rehabil 1998 May-Jun;19(3):210-2. doi: 10.1097/00004630-199805000-00004. PMID: 9622463
Brain abscess caused by Schizophyllum commune: an emerging basidiomycete pathogen.
Rihs JD, Padhye AA, Good CB
J Clin Microbiol 1996 Jul;34(7):1628-32. doi: 10.1128/JCM.34.7.1628-1632.1996. PMID: 8784558Free PMC Article
Inhalation injury.
Carrougher GJ
AACN Clin Issues Crit Care Nurs 1993 May;4(2):367-77. PMID: 8489883

Therapy

Lymphomatoid granulomatosis.
Roschewski M, Wilson WH
Cancer J 2012 Sep-Oct;18(5):469-74. doi: 10.1097/PPO.0b013e31826c5e19. PMID: 23006954
Pathophysiology of acute lung injury in combined burn and smoke inhalation injury.
Enkhbaatar P, Traber DL
Clin Sci (Lond) 2004 Aug;107(2):137-43. doi: 10.1042/CS20040135. PMID: 15151496
Diffuse alveolar hemorrhage in pediatric hematopoietic cell transplant patients.
Heggen J, West C, Olson E, Olson T, Teague G, Fortenberry J, Yeager AM
Pediatrics 2002 May;109(5):965-71. doi: 10.1542/peds.109.5.965. PMID: 11986464
Reduction in mortality in pediatric patients with inhalation injury with aerosolized heparin/N-acetylcystine [correction of acetylcystine] therapy.
Desai MH, Mlcak R, Richardson J, Nichols R, Herndon DN
J Burn Care Rehabil 1998 May-Jun;19(3):210-2. doi: 10.1097/00004630-199805000-00004. PMID: 9622463
Brain abscess caused by Schizophyllum commune: an emerging basidiomycete pathogen.
Rihs JD, Padhye AA, Good CB
J Clin Microbiol 1996 Jul;34(7):1628-32. doi: 10.1128/JCM.34.7.1628-1632.1996. PMID: 8784558Free PMC Article

Prognosis

Lepirudin in heparin-induced thrombocytopenia and extracorporeal membranous oxygenation.
Dager WE, Gosselin RC, Yoshikawa R, Owings JT
Ann Pharmacother 2004 Apr;38(4):598-601. Epub 2004 Feb 24 doi: 10.1345/aph.1D436. PMID: 14982973
Pulmonary transplantation for advanced bronchioloalveolar carcinoma.
Zorn GL Jr, McGiffin DC, Young KR Jr, Alexander CB, Weill D, Kirklin JK
J Thorac Cardiovasc Surg 2003 Jan;125(1):45-8. doi: 10.1067/mtc.2003.72. PMID: 12538984
Brain abscess caused by Schizophyllum commune: an emerging basidiomycete pathogen.
Rihs JD, Padhye AA, Good CB
J Clin Microbiol 1996 Jul;34(7):1628-32. doi: 10.1128/JCM.34.7.1628-1632.1996. PMID: 8784558Free PMC Article
Cranio-cervical decompression for Chiari I malformation. A retrospective evaluation of functional outcome with particular attention to the motor deficits.
Cristante L, Westphal M, Herrmann HD
Acta Neurochir (Wien) 1994;130(1-4):94-100. doi: 10.1007/BF01405508. PMID: 7725949
Determination of operability in candidates who undergo lung resection for bronchogenic carcinoma.
Murphy TP, Casey MT
Can J Surg 1990 Dec;33(6):470-3. PMID: 2253125

Clinical prediction guides

Idiopathic pneumonia syndrome after high-dose chemotherapy and autologous hematopoietic stem cell transplantation for high-risk breast cancer.
Wong R, Rondon G, Saliba RM, Shannon VR, Giralt SA, Champlin RE, Ueno NT
Bone Marrow Transplant 2003 Jun;31(12):1157-63. doi: 10.1038/sj.bmt.1704141. PMID: 12796796
Determination of operability in candidates who undergo lung resection for bronchogenic carcinoma.
Murphy TP, Casey MT
Can J Surg 1990 Dec;33(6):470-3. PMID: 2253125

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