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Deafness, autosomal dominant, with peripheral neuropathy

MedGen UID:
460102
Concept ID:
C3148751
Disease or Syndrome
Synonym: DEAFNESS, AUTOSOMAL DOMINANT, WITH PERIPHERAL NEUROPATHY
 
OMIM®: 603324

Professional guidelines

PubMed

Tonsgard JH
Semin Pediatr Neurol 2006 Mar;13(1):2-7. doi: 10.1016/j.spen.2006.01.005. PMID: 16818170

Recent clinical studies

Etiology

Finsterer J, Löscher W, Quasthoff S, Wanschitz J, Auer-Grumbach M, Stevanin G
J Neurol Sci 2012 Jul 15;318(1-2):1-18. Epub 2012 May 1 doi: 10.1016/j.jns.2012.03.025. PMID: 22554690
Auer-Grumbach M
Orphanet J Rare Dis 2008 Mar 18;3:7. doi: 10.1186/1750-1172-3-7. PMID: 18348718Free PMC Article
Kovach MJ, Campbell KC, Herman K, Waggoner B, Gelber D, Hughes LF, Kimonis VE
Am J Med Genet 2002 Apr 1;108(4):295-303. doi: 10.1002/ajmg.10223. PMID: 11920834
Nicholson GA, Dawkins JL, Blair IP, Kennerson ML, Gordon MJ, Cherryson AK, Nash J, Bananis T
Nat Genet 1996 May;13(1):101-4. doi: 10.1038/ng0596-101. PMID: 8673084
Thomas PK
J Med Genet 1975 Dec;12(4):317-26. doi: 10.1136/jmg.12.4.317. PMID: 176361Free PMC Article

Diagnosis

Beaudoux O, Lebre AS, Doco Fenzy M, Spodenkiewicz M, Canivet E, Colosio C, Poirsier C
Am J Med Genet A 2021 Mar;185(3):937-944. Epub 2021 Jan 13 doi: 10.1002/ajmg.a.62050. PMID: 33438842
Conboy E, Dhamija R, Wang M, Xie J, Dyck PJ, Bridges AG, Spinner RJ, Clayton AC, Watson RE, Messiaen L, Babovic-Vuksanovic D
J Med Genet 2016 Feb;53(2):123-6. Epub 2015 Sep 2 doi: 10.1136/jmedgenet-2015-103177. PMID: 26337637
Finsterer J, Löscher W, Quasthoff S, Wanschitz J, Auer-Grumbach M, Stevanin G
J Neurol Sci 2012 Jul 15;318(1-2):1-18. Epub 2012 May 1 doi: 10.1016/j.jns.2012.03.025. PMID: 22554690
Bennett CL, Lawson VH, Brickell KL, Isaacs K, Seltzer W, Lipe HP, Weiss MD, Carter GT, Flanigan KM, Chance PF, Bird TD
Neurology 2008 Jul 1;71(1):14-20. Epub 2008 May 21 doi: 10.1212/01.wnl.0000304048.94023.73. PMID: 18495953
Auer-Grumbach M
Orphanet J Rare Dis 2008 Mar 18;3:7. doi: 10.1186/1750-1172-3-7. PMID: 18348718Free PMC Article

Therapy

Franco-Hernández JA, Muñoz Rodríguez L, Ortiz de Landázuri PJ, García Hernández A
Braz J Anesthesiol 2013 Jan;63(1):113-5. Epub 2013 Aug 7 doi: 10.1016/j.bjane.2012.05.002. PMID: 24565095
Maljevic S, Wuttke TV, Lerche H
J Physiol 2008 Apr 1;586(7):1791-801. Epub 2008 Jan 31 doi: 10.1113/jphysiol.2008.150656. PMID: 18238816Free PMC Article

Prognosis

Postiglione E, Antelmi E, Pizza F, Vandi S, La Morgia C, Carelli V, Nassetti S, Seri M, Plazzi G
J Clin Sleep Med 2020 Jan 15;16(1):143-147. Epub 2019 Dec 6 doi: 10.5664/jcsm.8140. PMID: 31957642Free PMC Article
Walker LA, Bourque P, Smith AM, Warman Chardon J
Neuropsychology 2017 Mar;31(3):292-303. Epub 2016 Nov 21 doi: 10.1037/neu0000322. PMID: 27869457
Auer-Grumbach M
Orphanet J Rare Dis 2008 Mar 18;3:7. doi: 10.1186/1750-1172-3-7. PMID: 18348718Free PMC Article
Kovach MJ, Campbell KC, Herman K, Waggoner B, Gelber D, Hughes LF, Kimonis VE
Am J Med Genet 2002 Apr 1;108(4):295-303. doi: 10.1002/ajmg.10223. PMID: 11920834
Kovach MJ, Lin JP, Boyadjiev S, Campbell K, Mazzeo L, Herman K, Rimer LA, Frank W, Llewellyn B, Jabs EW, Gelber D, Kimonis VE
Am J Hum Genet 1999 Jun;64(6):1580-93. doi: 10.1086/302420. PMID: 10330345Free PMC Article

Clinical prediction guides

Kikuchi JK, Nagashima Y, Mano T, Ishiura H, Hayashi T, Shimizu J, Matsukawa T, Ichikawa Y, Takahashi Y, Karino S, Kanbayashi T, Kira J, Goto J, Tsuji S
J Mol Neurosci 2021 Sep;71(9):1796-1801. Epub 2021 Jan 12 doi: 10.1007/s12031-020-01784-5. PMID: 33433851
Napolitano F, Terracciano C, Bruno G, Nesti C, Barillari MR, Barillari U, Santorelli FM, Melone MAB, Esposito T, Sampaolo S
Am J Med Genet A 2020 Jan;182(1):176-182. Epub 2019 Oct 14 doi: 10.1002/ajmg.a.61381. PMID: 31609081
Conboy E, Dhamija R, Wang M, Xie J, Dyck PJ, Bridges AG, Spinner RJ, Clayton AC, Watson RE, Messiaen L, Babovic-Vuksanovic D
J Med Genet 2016 Feb;53(2):123-6. Epub 2015 Sep 2 doi: 10.1136/jmedgenet-2015-103177. PMID: 26337637
Moghadam KK, Pizza F, La Morgia C, Franceschini C, Tonon C, Lodi R, Barboni P, Seri M, Ferrari S, Liguori R, Donadio V, Parchi P, Cornelio F, Inzitari D, Mignarri A, Capocchi G, Dotti MT, Winkelmann J, Lin L, Mignot E, Carelli V, Plazzi G
Brain 2014 Jun;137(Pt 6):1643-55. Epub 2014 Apr 10 doi: 10.1093/brain/awu069. PMID: 24727570
Auer-Grumbach M
Orphanet J Rare Dis 2008 Mar 18;3:7. doi: 10.1186/1750-1172-3-7. PMID: 18348718Free PMC Article

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