Calciphylaxis cutis

MedGen UID:: 900547
•Concept ID:: C4274083
•: Disease or Syndrome

Synonym:	calciphylaxis cutis
SNOMED CT:	Calciphylaxis cutis (717043006)

Monarch Initiative:	MONDO:0017216
Orphanet:	ORPHA280065

Definition

A life-threatening syndrome with manifestation of progressive and painful skin ulcerations associated with calcification of medium-size and small cutaneous arterial vessels. It affects mainly patients on dialysis or after renal transplantation. [from SNOMEDCT_US]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVCalciphylaxis cutis

Phenotypic abnormality
- Abnormality of the musculoskeletal system
  - Abnormality of the musculature
    - Abnormal skeletal muscle morphology
      - Calcinosis
        Calciphylaxis
        Calciphylaxis cutis

Professional guidelines

PubMed

Differential diagnosis of calciphylaxis in chronic dialysis patients.

Musso CG, Enz PA, Kowalczuk A, Cozzolino M, Brandenburg V, Nigwekar S
Int Urol Nephrol 2020 Mar;52(3):595-597. Epub 2020 Feb 1 doi: 10.1007/s11255-020-02388-z. PMID: 32008200

Atypical wounds. Best clinical practice and challenges.

Isoherranen K, O'Brien JJ, Barker J, Dissemond J, Hafner J, Jemec GBE, Kamarachev J, Läuchli S, Montero EC, Nobbe S, Sunderkötter C, Velasco ML
J Wound Care 2019 Jun 1;28(Sup6):S1-S92. doi: 10.12968/jowc.2019.28.Sup6.S1. PMID: 31169055

Calciphylaxis: Diagnosis, Pathogenesis, and Treatment.

Chang JJ
Adv Skin Wound Care 2019 May;32(5):205-215. doi: 10.1097/01.ASW.0000554443.14002.13. PMID: 31008757

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