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Lipoblastomatosis

MedGen UID:
83154
•Concept ID:
C0334475
•
Neoplastic Process
Synonym: Lipoblastomatoses
SNOMED CT: Lipoblastomatosis (63629005); Fetal lipomatosis (63629005); Lipoblastomatosis (400149007); Fetal lipomatosis (400149007); Lipoblastoma/lipoblastomatosis (421098004); Lipoblastoma AND/OR lipoblastomatosis (63629005); Foetal lipomatosis (400149007); Foetal lipoma (63629005); Foetal lipomatosis (63629005)

Definition

A neoplastic process characterized by the presence of multiple lipoblastomas. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLipoblastomatosis

Professional guidelines

PubMed

Analysis of diagnosis and treatment of lipoblastomatosis.
Mo Z, Xie X, Wang H, Qin H, Han W, Li X
Sci China Life Sci 2017 Jul;60(7):778-780. Epub 2017 Jun 16 doi: 10.1007/s11427-017-9088-6. PMID: 28639103

Recent clinical studies

Etiology

Mesenteric lipoblastomatosis: an uncommon fat-containing childhood tumour diagnosed on imaging.
Yadav R, Kandasamy D, Agarwal S, Gamanagatti S
BMJ Case Rep 2023 May 26;16(5) doi: 10.1136/bcr-2022-249928. PMID: 37236672Free PMC Article
Follow-up outcomes of pediatric patients who underwent surgical resection for lipoblastomas or lipoblastomatosis: a single-institution experience with a systematic review and meta-analysis.
Dao D, Najor AJ, Sun PY, Farrokhyar F, Moir CR, Ishitani MB
Pediatr Surg Int 2020 Mar;36(3):341-355. Epub 2020 Jan 14 doi: 10.1007/s00383-019-04612-z. PMID: 31938836
A rare case of inguinolabial lipoblastoma in a 13-month-old female.
Kirkham YA, Yarbrough CM, Pippi Salle JL, Allen LM
J Pediatr Urol 2013 Feb;9(1):e64-7. Epub 2012 Oct 25 doi: 10.1016/j.jpurol.2012.08.007. PMID: 23103129
Lipoblastoma and lipoblastomatosis.
Bourelle S, Viehweger E, Launay F, Quilichini B, Bouvier C, Hagemeijer A, Jouve JL, Bollini G
J Pediatr Orthop B 2006 Sep;15(5):356-61. doi: 10.1097/01202412-200609000-00010. PMID: 16891964
Lipoblastoma of infancy mimicking hemangioma of infancy.
Steckman D, Zide B, Greco MA, Rivera R, Blei F
Arch Facial Plast Surg 2005 Sep-Oct;7(5):326-30. doi: 10.1001/archfaci.7.5.326. PMID: 16172343

Diagnosis

Mesenteric lipoblastomatosis: an uncommon fat-containing childhood tumour diagnosed on imaging.
Yadav R, Kandasamy D, Agarwal S, Gamanagatti S
BMJ Case Rep 2023 May 26;16(5) doi: 10.1136/bcr-2022-249928. PMID: 37236672Free PMC Article
Rare retro peritoneal tumor in infants.
Ben Hassine L, Douira W, Lahmar L, Louati H, Bellagha I
Tunis Med 2018 Jun;96(6):339-342. PMID: 30430470
Lipoblastomatosis of the retropharyngeal space: pathogenesis, presentation, and management, with a focus on head-neck lipoblastoma(toses).
M D, S K, S R, S Mukhopadhya
B-ENT 2016;12(1):33-9. PMID: 27097392
Lipoblastomatosis appearing as an unusual symmetric upper lip deformity.
Morioka D, Amikura Y
J Plast Reconstr Aesthet Surg 2011 Dec;64(12):1669-71. Epub 2011 Jul 23 doi: 10.1016/j.bjps.2011.05.028. PMID: 21784719
Lipoblastomatosis of the neck causing hemiparesis: a case report and review of the literature.
Sun JJ, Rasgon BM, Hilsinger RL Jr
Head Neck 2003 Apr;25(4):337-40. doi: 10.1002/hed.10176. PMID: 12658739

Therapy

Follow-up outcomes of pediatric patients who underwent surgical resection for lipoblastomas or lipoblastomatosis: a single-institution experience with a systematic review and meta-analysis.
Dao D, Najor AJ, Sun PY, Farrokhyar F, Moir CR, Ishitani MB
Pediatr Surg Int 2020 Mar;36(3):341-355. Epub 2020 Jan 14 doi: 10.1007/s00383-019-04612-z. PMID: 31938836
Cervical epidural lipoblastomatosis: changing MR appearance after chemotherapy.
Kamel HA, Brennan PR, Farrell MA
AJNR Am J Neuroradiol 1999 Mar;20(3):386-9. PMID: 10219402Free PMC Article

Prognosis

Lipoblastomatosis Extended into the Lumbar Spinal Canal in a Child: A Case Report.
Saga M, Yamaura A, Miyagawa T
Pediatr Neurosurg 2023;58(3):168-172. Epub 2023 Jun 14 doi: 10.1159/000531548. PMID: 37315552
Follow-up outcomes of pediatric patients who underwent surgical resection for lipoblastomas or lipoblastomatosis: a single-institution experience with a systematic review and meta-analysis.
Dao D, Najor AJ, Sun PY, Farrokhyar F, Moir CR, Ishitani MB
Pediatr Surg Int 2020 Mar;36(3):341-355. Epub 2020 Jan 14 doi: 10.1007/s00383-019-04612-z. PMID: 31938836
Giant abdomino-pelvic adipose tumors of childhood.
Cascini V, Lisi G, Lauriti G, Sindici G, Chiesa PL
Pediatr Surg Int 2012 Jan;28(1):89-93. Epub 2011 Aug 30 doi: 10.1007/s00383-011-2971-8. PMID: 21877241
Omental lipoblastoma.
Mallick MS
J Ayub Med Coll Abbottabad 2007 Oct-Dec;19(4):134-5. PMID: 18693617
Lipoblastoma of infancy mimicking hemangioma of infancy.
Steckman D, Zide B, Greco MA, Rivera R, Blei F
Arch Facial Plast Surg 2005 Sep-Oct;7(5):326-30. doi: 10.1001/archfaci.7.5.326. PMID: 16172343

Clinical prediction guides

Lipoblastomatosis Extended into the Lumbar Spinal Canal in a Child: A Case Report.
Saga M, Yamaura A, Miyagawa T
Pediatr Neurosurg 2023;58(3):168-172. Epub 2023 Jun 14 doi: 10.1159/000531548. PMID: 37315552
Pediatric lipoblastoma in the head and neck: a systematic review of 48 reported cases.
Pham NS, Poirier B, Fuller SC, Dublin AB, Tollefson TT
Int J Pediatr Otorhinolaryngol 2010 Jul;74(7):723-8. Epub 2010 May 15 doi: 10.1016/j.ijporl.2010.04.010. PMID: 20472310
Case report 675: Lipoblastoma of knee.
Ehara S, Tokunaga S, Monma N, Satoh T, Tamakawa Y, Abe M
Skeletal Radiol 1991;20(4):319-21. doi: 10.1007/BF02341676. PMID: 1853230
Benign lipoblastoma: first case report of a mesenteric origin.
Zanetti G
Tumori 1988 Aug 31;74(4):495-8. doi: 10.1177/030089168807400420. PMID: 3188249
Lipoblastomatosis: a tumor of fetal fat different from hibernoma; report of a case, with observations on the embryogenesis of human adipose tissue.
VELLIOS F, BAEZ J, SHUMACKER HB
Am J Pathol 1958 Nov-Dec;34(6):1149-59. PMID: 13583102Free PMC Article

Recent systematic reviews

Follow-up outcomes of pediatric patients who underwent surgical resection for lipoblastomas or lipoblastomatosis: a single-institution experience with a systematic review and meta-analysis.
Dao D, Najor AJ, Sun PY, Farrokhyar F, Moir CR, Ishitani MB
Pediatr Surg Int 2020 Mar;36(3):341-355. Epub 2020 Jan 14 doi: 10.1007/s00383-019-04612-z. PMID: 31938836
Pediatric lipoblastoma in the head and neck: a systematic review of 48 reported cases.
Pham NS, Poirier B, Fuller SC, Dublin AB, Tollefson TT
Int J Pediatr Otorhinolaryngol 2010 Jul;74(7):723-8. Epub 2010 May 15 doi: 10.1016/j.ijporl.2010.04.010. PMID: 20472310

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