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Ataxia neuropathy spectrum

MedGen UID:
777176
Concept ID:
C3683791
Disease or Syndrome
Synonyms: Ataxia Neuropathy Spectrum; SANDO; Sensory Ataxia Neuropathy Dysarthria and Ophthalmoplegia
 
Monarch Initiative: MONDO:0016798
Orphanet: ORPHA254818

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAtaxia neuropathy spectrum

Professional guidelines

PubMed

Kierdaszuk B, Kaliszewska M, Rusecka J, Kosińska J, Bartnik E, Tońska K, Kamińska AM, Kostera-Pruszczyk A
Genes (Basel) 2020 Dec 31;12(1) doi: 10.3390/genes12010054. PMID: 33396418Free PMC Article

Recent clinical studies

Etiology

Kierdaszuk B, Kaliszewska M, Rusecka J, Kosińska J, Bartnik E, Tońska K, Kamińska AM, Kostera-Pruszczyk A
Genes (Basel) 2020 Dec 31;12(1) doi: 10.3390/genes12010054. PMID: 33396418Free PMC Article
Wong LJ, Naviaux RK, Brunetti-Pierri N, Zhang Q, Schmitt ES, Truong C, Milone M, Cohen BH, Wical B, Ganesh J, Basinger AA, Burton BK, Swoboda K, Gilbert DL, Vanderver A, Saneto RP, Maranda B, Arnold G, Abdenur JE, Waters PJ, Copeland WC
Hum Mutat 2008 Sep;29(9):E150-72. doi: 10.1002/humu.20824. PMID: 18546365Free PMC Article

Diagnosis

Jha R, Patel H, Dubey R, Goswami JN, Bhagwat C, Saini L, K Manokaran R, John BM, Kovilapu UB, Mohimen A, Saxena A, Sondhi V
J Child Neurol 2022 Mar;37(4):246-255. Epub 2022 Jan 5 doi: 10.1177/08830738211067065. PMID: 34986040
Baty K, Farrugia ME, Hopton S, Falkous G, Schaefer AM, Stewart W, Willison HJ, Reilly MM, Blakely EL, Taylor RW, Ng YS
Neuromuscul Disord 2021 Nov;31(11):1186-1193. Epub 2021 Jun 4 doi: 10.1016/j.nmd.2021.05.014. PMID: 34325999Free PMC Article
Rahman S, Copeland WC
Nat Rev Neurol 2019 Jan;15(1):40-52. doi: 10.1038/s41582-018-0101-0. PMID: 30451971Free PMC Article
Lovan A, Ihtsham ul Haq, Balakrishnan N
BMJ Case Rep 2013 Aug 30;2013 doi: 10.1136/bcr-2013-010343. PMID: 23997076Free PMC Article
Wong LJ, Naviaux RK, Brunetti-Pierri N, Zhang Q, Schmitt ES, Truong C, Milone M, Cohen BH, Wical B, Ganesh J, Basinger AA, Burton BK, Swoboda K, Gilbert DL, Vanderver A, Saneto RP, Maranda B, Arnold G, Abdenur JE, Waters PJ, Copeland WC
Hum Mutat 2008 Sep;29(9):E150-72. doi: 10.1002/humu.20824. PMID: 18546365Free PMC Article

Therapy

Shi H, Waldman G, Tobochnik S, Kuo SH, Pack A
Neurology 2019 May 14;92(20):968-972. doi: 10.1212/WNL.0000000000007507. PMID: 31085725Free PMC Article
Finsterer J, Zarrouk Mahjoub S
Seizure 2012 Jun;21(5):316-21. Epub 2012 Mar 27 doi: 10.1016/j.seizure.2012.03.003. PMID: 22459315

Prognosis

Wong LJ, Naviaux RK, Brunetti-Pierri N, Zhang Q, Schmitt ES, Truong C, Milone M, Cohen BH, Wical B, Ganesh J, Basinger AA, Burton BK, Swoboda K, Gilbert DL, Vanderver A, Saneto RP, Maranda B, Arnold G, Abdenur JE, Waters PJ, Copeland WC
Hum Mutat 2008 Sep;29(9):E150-72. doi: 10.1002/humu.20824. PMID: 18546365Free PMC Article

Clinical prediction guides

Weiland D, Brachvogel B, Hornig-Do HT, Neuhaus JFG, Holzer T, Tobin DJ, Niessen CM, Wiesner RJ, Baris OR
J Invest Dermatol 2018 Jan;138(1):132-140. Epub 2017 Sep 1 doi: 10.1016/j.jid.2017.08.019. PMID: 28867657
Bostan A, Glibert G, Dachy B, Dan B
Auton Neurosci 2012 Sep 25;170(1-2):70-2. Epub 2012 Jul 16 doi: 10.1016/j.autneu.2012.06.002. PMID: 22805437
Wong LJ, Naviaux RK, Brunetti-Pierri N, Zhang Q, Schmitt ES, Truong C, Milone M, Cohen BH, Wical B, Ganesh J, Basinger AA, Burton BK, Swoboda K, Gilbert DL, Vanderver A, Saneto RP, Maranda B, Arnold G, Abdenur JE, Waters PJ, Copeland WC
Hum Mutat 2008 Sep;29(9):E150-72. doi: 10.1002/humu.20824. PMID: 18546365Free PMC Article

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