U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Dermal Nerve Sheath Myxoma

MedGen UID:
698545
•Concept ID:
C1275265
•
Neoplastic Process
Synonyms: Classic Variant of Neurothekeoma; Dermal nerve sheath myxoma; Dermal neurothekeoma; Myxoid Variant of Neurothekeoma
SNOMED CT: Dermal nerve sheath myxoma (404034009); Dermal neurothekeoma (404034009)

Definition

A usually painless, slow growing benign tumor that most often arises from the extremities. It is characterized by the presence of abundant myxoid matrix and small epithelioid neoplastic Schwann cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVDermal Nerve Sheath Myxoma

Recent clinical studies

Etiology

Podoplanin expression in fibrous histiocytomas and cellular neurothekeomas.
Kaddu S, Leinweber B
Am J Dermatopathol 2009 Apr;31(2):137-9. doi: 10.1097/DAD.0b013e31819821c7. PMID: 19318798
Superficial angiomyxoma: clinicopathologic analysis of a series of distinctive but poorly recognized cutaneous tumors with tendency for recurrence.
Calonje E, Guerin D, McCormick D, Fletcher CD
Am J Surg Pathol 1999 Aug;23(8):910-7. doi: 10.1097/00000478-199908000-00008. PMID: 10435560

Diagnosis

Podoplanin expression in fibrous histiocytomas and cellular neurothekeomas.
Kaddu S, Leinweber B
Am J Dermatopathol 2009 Apr;31(2):137-9. doi: 10.1097/DAD.0b013e31819821c7. PMID: 19318798
Superficial angiomyxoma: clinicopathologic analysis of a series of distinctive but poorly recognized cutaneous tumors with tendency for recurrence.
Calonje E, Guerin D, McCormick D, Fletcher CD
Am J Surg Pathol 1999 Aug;23(8):910-7. doi: 10.1097/00000478-199908000-00008. PMID: 10435560
Dermal nerve sheath myxoma: a study of three cases.
Fletcher CD, Chan JK, McKee PH
Histopathology 1986 Feb;10(2):135-45. doi: 10.1111/j.1365-2559.1986.tb02469.x. PMID: 3082736

Clinical prediction guides

Podoplanin expression in fibrous histiocytomas and cellular neurothekeomas.
Kaddu S, Leinweber B
Am J Dermatopathol 2009 Apr;31(2):137-9. doi: 10.1097/DAD.0b013e31819821c7. PMID: 19318798

Supplemental Content

Table of contents

    Related information

    • PubMed
      Related literature resources in PubMed

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...