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Myxosarcoma

MedGen UID:
6508
Concept ID:
C0027155
Neoplastic Process
Synonym: Myxosarcomas
SNOMED CT: Myxosarcoma (28351005)
 
Monarch Initiative: MONDO:0006863

Definition

An infiltrating malignant soft tissue neoplasm characterized by the presence of immature undifferentiated cells and abundant myxoid stroma formation. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMyxosarcoma

Professional guidelines

PubMed

Duffy GP, Wood MB, Rock MG, Sim FH
J Bone Joint Surg Am 2000 Apr;82(4):544-54. doi: 10.2106/00004623-200004000-00009. PMID: 10761944

Recent clinical studies

Etiology

Dadrass F, Gusho C, Yang F, Culvern C, Bloom J, Fillingham Y, Colman M, Gitelis S, Blank A
J Surg Oncol 2021 Feb;123(2):489-496. Epub 2020 Oct 30 doi: 10.1002/jso.26277. PMID: 33125727
Shimoda H, Yonezawa K, Shinomiya H, Otsuki N, Hashikawa K, Sasaki R, Komura E, Nibu KI
Head Neck 2016 Dec;38(12):E2519-E2522. Epub 2016 Aug 8 doi: 10.1002/hed.24558. PMID: 27501198
Michal M, Kazakov DV, Hadravský L, Kinkor Z, Kuroda N, Michal M
Ann Diagn Pathol 2015 Jun;19(3):157-63. Epub 2015 Apr 6 doi: 10.1016/j.anndiagpath.2015.03.012. PMID: 25886867
Dulou R, Chargari C, Dagain A, Teriitehau C, Goasguen O, Jeanjean O, Védrine L
Neurol Neurochir Pol 2012 Jan-Feb;46(1):76-81. doi: 10.5114/ninp.2012.27176. PMID: 22426765
Attum AA, Johnson GS, Masri Z, Girardet R, Lansing AM
Ann Thorac Surg 1987 Aug;44(2):217-22. doi: 10.1016/s0003-4975(10)62052-8. PMID: 3304181

Diagnosis

Lucas DR
Arch Pathol Lab Med 2017 Nov;141(11):1503-1507. doi: 10.5858/arpa.2017-0219-RA. PMID: 29072951
de Castro BA, Piancastelli AC, Meyer RL, Piancastelli PM, Ribeiro CA, Miranda RM
An Bras Dermatol 2016 Jan-Feb;91(1):97-9. doi: 10.1590/abd1806-4841.20163922. PMID: 26982788Free PMC Article
Qiubei Z, Cheng L, Yaping X, Shunzhang L, Jingping F
World J Surg Oncol 2012 Nov 15;10:245. doi: 10.1186/1477-7819-10-245. PMID: 23152982Free PMC Article
Clarke LE
Dermatol Clin 2012 Oct;30(4):643-56, vi. Epub 2012 Aug 11 doi: 10.1016/j.det.2012.06.005. PMID: 23021051
MORGAN J, WELLS GC
Proc R Soc Med 1963 Oct;56(10):903. PMID: 14072145Free PMC Article

Therapy

Doshi SD, Oza J, Remotti H, Remotti F, Moy MP, Schwartz GK, Ingham M
JCO Precis Oncol 2021 Nov;5:1-5. doi: 10.1200/PO.20.00201. PMID: 34994591
Luo Y, Min L, Zhou Y, Tang F, Lu M, Xie H, Wang Y, Duan H, Zhang W, Tu C
Medicine (Baltimore) 2021 Mar 26;100(12):e25262. doi: 10.1097/MD.0000000000025262. PMID: 33761725Free PMC Article
Song HN, Kang MG, Park JR, Hwang JY, Kang JH, Lee WS, Lee GW
Cancer Res Treat 2018 Oct;50(4):1458-1461. Epub 2018 Jan 22 doi: 10.4143/crt.2017.529. PMID: 29361819Free PMC Article
Clarke LE
Dermatol Clin 2012 Oct;30(4):643-56, vi. Epub 2012 Aug 11 doi: 10.1016/j.det.2012.06.005. PMID: 23021051
Blodi FC
Am J Ophthalmol 1969 Sep;68(3):407-12. doi: 10.1016/0002-9394(69)90703-x. PMID: 5257914

Prognosis

Lucas DR
Arch Pathol Lab Med 2017 Nov;141(11):1503-1507. doi: 10.5858/arpa.2017-0219-RA. PMID: 29072951
Qiubei Z, Cheng L, Yaping X, Shunzhang L, Jingping F
World J Surg Oncol 2012 Nov 15;10:245. doi: 10.1186/1477-7819-10-245. PMID: 23152982Free PMC Article
Clarke LE
Dermatol Clin 2012 Oct;30(4):643-56, vi. Epub 2012 Aug 11 doi: 10.1016/j.det.2012.06.005. PMID: 23021051
Suzuki M, Doi H, Koshima R, Sugiki K, Kazui T, Ohno T
Gen Thorac Cardiovasc Surg 2011 Apr;59(4):284-7. Epub 2011 Apr 12 doi: 10.1007/s11748-010-0673-0. PMID: 21484557
Attum AA, Johnson GS, Masri Z, Girardet R, Lansing AM
Ann Thorac Surg 1987 Aug;44(2):217-22. doi: 10.1016/s0003-4975(10)62052-8. PMID: 3304181

Clinical prediction guides

Dadrass F, Gusho C, Yang F, Culvern C, Bloom J, Fillingham Y, Colman M, Gitelis S, Blank A
J Surg Oncol 2021 Feb;123(2):489-496. Epub 2020 Oct 30 doi: 10.1002/jso.26277. PMID: 33125727
Srivastava P, Husain N, Neyaz A, Gupta V
BMJ Case Rep 2018 Jul 18;2018 doi: 10.1136/bcr-2018-224259. PMID: 30021730Free PMC Article
Vallejo-Benítez A, Rodríguez-Zarco E, Carrasco SP, Pereira-Gallardo S, Brugal Molina J, García-Escudero A, Robles Frías A, Marcilla D, González-Cámpora R
Ann Diagn Pathol 2017 Oct;30:8-11. Epub 2017 May 11 doi: 10.1016/j.anndiagpath.2017.05.002. PMID: 28965630
Soo A, Molloy F, Herron B, Parissis H
Asian Cardiovasc Thorac Ann 2014 Jun;22(5):611-3. Epub 2013 Oct 3 doi: 10.1177/0218492313480156. PMID: 24867039
Kim YC, Vandersteen DP, Jung HG
Am J Dermatopathol 2005 Feb;27(1):51-5. doi: 10.1097/01.dad.0000141547.31306.4e. PMID: 15677980

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