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Orbit sarcoma

MedGen UID:
277449
Concept ID:
C1335131
Neoplastic Process
Synonyms: orbit of skull sarcoma; Orbit Sarcoma; orbit sarcoma; Orbital Sarcoma; orbital sarcoma; Sarcoma of orbit; Sarcoma of Orbit; sarcoma of orbit; sarcoma of orbit of skull; Sarcoma of the Orbit; sarcoma of the orbit
SNOMED CT: Sarcoma of orbit (699354006)
 
Monarch Initiative: MONDO:0004943

Definition

A malignant soft tissue neoplasm that arises from the structures of the orbit. The majority of the cases are rhabdomyosarcomas. [from NCI]

Professional guidelines

PubMed

Koka K, Rahim FE, El-Hadad C, Bell D, Debnam JM, Guo Y, Esmaeli B
Head Neck 2021 Dec;43(12):3857-3865. Epub 2021 Oct 10 doi: 10.1002/hed.26884. PMID: 34632670

Recent clinical studies

Etiology

Kuan EC, Wang EW, Adappa ND, Beswick DM, London NR Jr, Su SY, Wang MB, Abuzeid WM, Alexiev B, Alt JA, Antognoni P, Alonso-Basanta M, Batra PS, Bhayani M, Bell D, Bernal-Sprekelsen M, Betz CS, Blay JY, Bleier BS, Bonilla-Velez J, Callejas C, Carrau RL, Casiano RR, Castelnuovo P, Chandra RK, Chatzinakis V, Chen SB, Chiu AG, Choby G, Chowdhury NI, Citardi MJ, Cohen MA, Dagan R, Dalfino G, Dallan I, Dassi CS, de Almeida J, Dei Tos AP, DelGaudio JM, Ebert CS, El-Sayed IH, Eloy JA, Evans JJ, Fang CH, Farrell NF, Ferrari M, Fischbein N, Folbe A, Fokkens WJ, Fox MG, Lund VJ, Gallia GL, Gardner PA, Geltzeiler M, Georgalas C, Getz AE, Govindaraj S, Gray ST, Grayson JW, Gross BA, Grube JG, Guo R, Ha PK, Halderman AA, Hanna EY, Harvey RJ, Hernandez SC, Holtzman AL, Hopkins C, Huang Z, Huang Z, Humphreys IM, Hwang PH, Iloreta AM, Ishii M, Ivan ME, Jafari A, Kennedy DW, Khan M, Kimple AJ, Kingdom TT, Knisely A, Kuo YJ, Lal D, Lamarre ED, Lan MY, Le H, Lechner M, Lee NY, Lee JK, Lee VH, Levine CG, Lin JC, Lin DT, Lobo BC, Locke T, Luong AU, Magliocca KR, Markovic SN, Matnjani G, McKean EL, Meço C, Mendenhall WM, Michel L, Na'ara S, Nicolai P, Nuss DW, Nyquist GG, Oakley GM, Omura K, Orlandi RR, Otori N, Papagiannopoulos P, Patel ZM, Pfister DG, Phan J, Psaltis AJ, Rabinowitz MR, Ramanathan M Jr, Rimmer R, Rosen MR, Sanusi O, Sargi ZB, Schafhausen P, Schlosser RJ, Sedaghat AR, Senior BA, Shrivastava R, Sindwani R, Smith TL, Smith KA, Snyderman CH, Solares CA, Sreenath SB, Stamm A, Stölzel K, Sumer B, Surda P, Tajudeen BA, Thompson LDR, Thorp BD, Tong CCL, Tsang RK, Turner JH, Turri-Zanoni M, Udager AM, van Zele T, VanKoevering K, Welch KC, Wise SK, Witterick IJ, Won TB, Wong SN, Woodworth BA, Wormald PJ, Yao WC, Yeh CF, Zhou B, Palmer JN
Int Forum Allergy Rhinol 2024 Feb;14(2):149-608. Epub 2024 Jan 2 doi: 10.1002/alr.23262. PMID: 37658764
Liu CK, Williamson JE 3rd, Milman T, Lally SE, Shields CL
Ophthalmic Plast Reconstr Surg 2022 Nov-Dec 01;38(6):e180-e183. Epub 2022 Jul 4 doi: 10.1097/IOP.0000000000002236. PMID: 35793663
Davies BW, Prescott CR, Said SA, Campana J, Attié-Castro FA, Velasco E Cruz AA, Durairaj VD
Ophthalmic Plast Reconstr Surg 2014 May-Jun;30(3):205-8. doi: 10.1097/IOP.0000000000000168. PMID: 24807535
Aerts I, Lumbroso-Le Rouic L, Gauthier-Villars M, Brisse H, Doz F, Desjardins L
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Char DH
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Diagnosis

Yamazaki D, Ogihara N, Horiuchi T
World Neurosurg 2020 Jul;139:604-607. Epub 2020 Apr 25 doi: 10.1016/j.wneu.2020.04.069. PMID: 32339743
Arora K, Riddle ND
Arch Pathol Lab Med 2018 Nov;142(11):1421-1424. doi: 10.5858/arpa.2017-0109-RS. PMID: 30407856
Kinori M, Ben Simon GJ, Zehavi-Dorin T, Robbins SL, Siatkowski RM
Surv Ophthalmol 2017 Mar-Apr;62(2):237-240. Epub 2016 Feb 26 doi: 10.1016/j.survophthal.2016.02.004. PMID: 26921808
Shields JA, Shields CL
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Volpe NJ, Jakobiec FA
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Therapy

Erickson BP, Tse DT
Surv Ophthalmol 2014 Jul-Aug;59(4):378-92. Epub 2013 Dec 3 doi: 10.1016/j.survophthal.2013.11.002. PMID: 24929905
Karcioglu ZA, Hadjistilianou D, Rozans M, DeFrancesco S
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Gane NF, Lindup R, Strickland P, Bennett MH
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Prognosis

Rodriguez-Beato F, De Jesus O, Sanchez-Ortiz J, Delgado P, Perez-Berenguer JL, Labat EJ
BMJ Case Rep 2021 Mar 4;14(3) doi: 10.1136/bcr-2020-240516. PMID: 33664037Free PMC Article
Arora K, Riddle ND
Arch Pathol Lab Med 2018 Nov;142(11):1421-1424. doi: 10.5858/arpa.2017-0109-RS. PMID: 30407856
Clair BC, Salloum G, Carruth BP, Bersani TA, Hill RH 3rd
Ophthalmic Plast Reconstr Surg 2018 Nov/Dec;34(6):e180-e182. doi: 10.1097/IOP.0000000000001219. PMID: 30204636
Davies BW, Prescott CR, Said SA, Campana J, Attié-Castro FA, Velasco E Cruz AA, Durairaj VD
Ophthalmic Plast Reconstr Surg 2014 May-Jun;30(3):205-8. doi: 10.1097/IOP.0000000000000168. PMID: 24807535
Yeniad B, Tuncer S, Peksayar G, Mete O, Minareci O
Ophthalmic Plast Reconstr Surg 2009 Mar-Apr;25(2):154-5. doi: 10.1097/IOP.0b013e31819aaef4. PMID: 19300170

Clinical prediction guides

Brown NJ, Bhatia K, Teague J, White SM, Lo P, Challis J, Beshay V, Sullivan M, Malkin D, Hansford JR
Fam Cancer 2019 Jan;18(1):101-104. doi: 10.1007/s10689-018-0087-1. PMID: 29737433
Torrado CS, Zaldibar NM, Velasco-Benito V, Fernández-Hermida R
J Craniofac Surg 2011 May;22(3):1139-41. doi: 10.1097/SCS.0b013e3182108fdd. PMID: 21586970
Aerts I, Lumbroso-Le Rouic L, Gauthier-Villars M, Brisse H, Doz F, Desjardins L
Orphanet J Rare Dis 2006 Aug 25;1:31. doi: 10.1186/1750-1172-1-31. PMID: 16934146Free PMC Article
Miyashita K, Abe Y, Osamura Y
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Recent systematic reviews

Eshraghi B, Jahanbani-Ardakani HR, Abtahi SM, Abtahi SH
J Fr Ophtalmol 2019 Oct;42(8):913-924. Epub 2019 Apr 10 doi: 10.1016/j.jfo.2018.11.012. PMID: 30981544
Su C, Peng C, Agbodza E, Bai HX, Huang Y, Karakousis G, Zhang PJ, Zhang Z
Medicine (Baltimore) 2018 Mar;97(9):e9823. doi: 10.1097/MD.0000000000009823. PMID: 29489679Free PMC Article
Tata A, Cohen-Inbar O, Sheehan JP
BMJ Case Rep 2016 Oct 7;2016 doi: 10.1136/bcr-2016-217114. PMID: 27758816Free PMC Article
Erickson BP, Tse DT
Surv Ophthalmol 2014 Jul-Aug;59(4):378-92. Epub 2013 Dec 3 doi: 10.1016/j.survophthal.2013.11.002. PMID: 24929905

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