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Peripheral Primitive Neuroectodermal Tumor of the Kidney

MedGen UID:
253780
•Concept ID:
C1134517
•
Neoplastic Process
Synonyms: Malignant Neuroepithelial Tumor of the Kidney; Neuroepithelial Tumor of the Kidney

Definition

A small round cell tumor with neural differentiation arising from the kidney. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPeripheral Primitive Neuroectodermal Tumor of the Kidney

Recent clinical studies

Etiology

The immune landscape of solid pediatric tumors.
Sherif S, Roelands J, Mifsud W, Ahmed EI, Raynaud CM, Rinchai D, Sathappan A, Maaz A, Saleh A, Ozer E, Fakhro KA, Mifsud B, Thorsson V, Bedognetti D, Hendrickx WRL
J Exp Clin Cancer Res 2022 Jun 11;41(1):199. doi: 10.1186/s13046-022-02397-z. PMID: 35690832Free PMC Article
Peripheral neuroblastic tumor of the kidney: case report and review of literature.
Moscheo C, Campari A, Podda MG, Riccipetitoni G, Collini P, Renne SL, Vella C, Napolitano M, Luksch R
Tumori 2018 Dec;104(6):NP34-NP37. Epub 2018 Jul 19 doi: 10.1177/0300891618788475. PMID: 30021475
Ewing sarcoma/primitive neuroectodermal tumor of the kidney: clinicopathologic analysis of 34 cases.
Karpate A, Menon S, Basak R, Yuvaraja TB, Tongaonkar HB, Desai SB
Ann Diagn Pathol 2012 Aug;16(4):267-74. Epub 2012 Apr 23 doi: 10.1016/j.anndiagpath.2011.07.011. PMID: 22534242
Neonatal renal tumours.
Powis M
Early Hum Dev 2010 Oct;86(10):607-12. doi: 10.1016/j.earlhumdev.2010.08.018. PMID: 20888153
The role of surgery in the treatment of neuroblastoma.
Kubota M
Surg Today 2010 Jun;40(6):526-32. Epub 2010 May 23 doi: 10.1007/s00595-009-4092-8. PMID: 20496133

Diagnosis

Primary Ewing sarcoma of the kidney: A series of four cases.
Patra S, Trivedi P
Malays J Pathol 2022 Apr;44(1):93-99. PMID: 35484891
Primary Paediatric Renal Primitive Neuroectodermal Tumor: A Case Report and Review of the Literature.
Khandakar B, Maiti M, Dey S, Ray PS, Bhattacharyya P, Sarkar R
Turk Patoloji Derg 2018;34(3):251-254. doi: 10.5146/tjpath.2015.01340. PMID: 28272661
Ewing Sarcoma/Primitive Neuroectodermal Tumor of the Kidney: A Rare and Lethal Entity.
Celli R, Cai G
Arch Pathol Lab Med 2016 Mar;140(3):281-5. doi: 10.5858/arpa.2014-0367-RS. PMID: 26927724
Neonatal renal tumours.
Powis M
Early Hum Dev 2010 Oct;86(10):607-12. doi: 10.1016/j.earlhumdev.2010.08.018. PMID: 20888153
Primitive neuroectodermal tumor of the kidney in a child.
Citak EC, Oguz A, Karadeniz C, Okur A, Akyurek N
Pediatr Hematol Oncol 2009 Oct-Nov;26(7):481-6. doi: 10.1080/08880010902754792. PMID: 19863203

Therapy

A rare entity of Primary Ewing sarcoma in kidney.
Cheng L, Xu Y, Song H, Huang H, Zhuo D
BMC Surg 2020 Nov 11;20(1):280. doi: 10.1186/s12893-020-00948-9. PMID: 33176766Free PMC Article
Primitive neuroectodermal tumors of kidney: Our experience in a tertiary care center.
Seth A, Mahapatra SK, Nayak B, Saini AK, Biswas B
Indian J Cancer 2016 Jan-Mar;53(1):109-12. doi: 10.4103/0019-509X.180854. PMID: 27146755
Primitive neuroectodermal tumor of the kidney in a child.
Citak EC, Oguz A, Karadeniz C, Okur A, Akyurek N
Pediatr Hematol Oncol 2009 Oct-Nov;26(7):481-6. doi: 10.1080/08880010902754792. PMID: 19863203
Long-term follow-up status of patients with neuroblastoma after undergoing either aggressive surgery or chemotherapy--a single institutional study.
Kubota M, Yagi M, Kanada S, Okuyama N, Kinoshita Y, Yamazaki S, Asami K, Ogawa A, Watanabe T
J Pediatr Surg 2004 Sep;39(9):1328-32. doi: 10.1016/j.jpedsurg.2004.05.012. PMID: 15359385
A para-testicular primitive neuroectodermal tumor in an adult: a case report and literature review.
Cohen DD, Zorn K, Bernard C, Rajan R, Kuzmarov IW
Can J Urol 2000 Aug;7(4):1081-4. PMID: 11109079

Prognosis

The immune landscape of solid pediatric tumors.
Sherif S, Roelands J, Mifsud W, Ahmed EI, Raynaud CM, Rinchai D, Sathappan A, Maaz A, Saleh A, Ozer E, Fakhro KA, Mifsud B, Thorsson V, Bedognetti D, Hendrickx WRL
J Exp Clin Cancer Res 2022 Jun 11;41(1):199. doi: 10.1186/s13046-022-02397-z. PMID: 35690832Free PMC Article
Primary Ewing sarcoma of the kidney: A series of four cases.
Patra S, Trivedi P
Malays J Pathol 2022 Apr;44(1):93-99. PMID: 35484891
Ewing Sarcoma/Primitive Neuroectodermal Tumor of the Kidney: A Rare and Lethal Entity.
Celli R, Cai G
Arch Pathol Lab Med 2016 Mar;140(3):281-5. doi: 10.5858/arpa.2014-0367-RS. PMID: 26927724
The role of surgery in the treatment of neuroblastoma.
Kubota M
Surg Today 2010 Jun;40(6):526-32. Epub 2010 May 23 doi: 10.1007/s00595-009-4092-8. PMID: 20496133
Primitive neuroectodermal tumor of the kidney in a child.
Citak EC, Oguz A, Karadeniz C, Okur A, Akyurek N
Pediatr Hematol Oncol 2009 Oct-Nov;26(7):481-6. doi: 10.1080/08880010902754792. PMID: 19863203

Clinical prediction guides

The immune landscape of solid pediatric tumors.
Sherif S, Roelands J, Mifsud W, Ahmed EI, Raynaud CM, Rinchai D, Sathappan A, Maaz A, Saleh A, Ozer E, Fakhro KA, Mifsud B, Thorsson V, Bedognetti D, Hendrickx WRL
J Exp Clin Cancer Res 2022 Jun 11;41(1):199. doi: 10.1186/s13046-022-02397-z. PMID: 35690832Free PMC Article
Initiation of immunotherapy with activated natural killer cells and anti-GD2 antibody dinutuximab prior to resection of primary neuroblastoma prolongs survival in mice.
Zobel MJ, Zamora AK, Wu HW, Sun J, Lascano D, Malvar J, Wang L, Sheard MA, Seeger RC, Kim ES
J Immunother Cancer 2020 Dec;8(2) doi: 10.1136/jitc-2020-001560. PMID: 33428582Free PMC Article
Diffusion-weighted MRI for differentiating Wilms tumor from neuroblastoma.
Aslan M, Aslan A, Arıöz Habibi H, Kalyoncu Uçar A, Özmen E, Bakan S, Kuruğoğlu S, Adaletli İ
Diagn Interv Radiol 2017 Sep-Oct;23(5):403-406. doi: 10.5152/dir.2017.16541. PMID: 28830846Free PMC Article
Examination of the distribution of the transferrin homologue, melanotransferrin (tumour antigen p97), in mouse and human.
Sekyere EO, Dunn LL, Richardson DR
Biochim Biophys Acta 2005 Mar 11;1722(2):131-42. Epub 2005 Jan 4 doi: 10.1016/j.bbagen.2004.12.002. PMID: 15716025
The role of fine needle aspiration in the assessment of renal masses.
Pilotti S, Rilke F, Alasio L, Garbagnati F
Acta Cytol 1988 Jan-Feb;32(1):1-10. PMID: 3336946

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