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Adult pleomorphic rhabdomyosarcoma

MedGen UID:
233966
•Concept ID:
C1332211
•
Neoplastic Process
Synonyms: Adult Pleomorphic Rhabdomyosarcoma; adult pleomorphic rhabdomyosarcoma; Pleomorphic rhabdomyosarcoma; pleomorphic rhabdomyosarcoma of adults; Pleomorphic rhabdomyosarcoma, adult type
SNOMED CT: Pleomorphic rhabdomyosarcoma (77455004); Pleomorphic rhabdomyosarcoma, adult type (77455004)
 
Monarch Initiative: MONDO:0004513

Definition

An aggressive rhabdomyosarcoma occurring in adults. The neoplasm is characterized by the presence of bizarre round, spindle, and polygonal cells. Clinical presentation includes a rapidly enlarging painful mass usually in the lower extremities. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdult pleomorphic rhabdomyosarcoma

Professional guidelines

PubMed

Impact of Rhabdomyosarcoma Treatment Modalities by Age in a Population-Based Setting.
Ferrari A, Bernasconi A, Bergamaschi L, Botta L, Andreano A, Castaing M, Rugge M, Bisogno G, Falcini F, Sacerdote C, Tagliabue G, Michiara M, Cirilli C, Barchielli A, Filiberti RA, Vitale MF, Tumino R, Stracci F, Chiaravalli S, Casanova M, Gasparini P, Milano GM, Gatta G, Trama A
J Adolesc Young Adult Oncol 2021 Jun;10(3):309-315. Epub 2020 Jul 30 doi: 10.1089/jayao.2020.0043. PMID: 32758055
Treatment Outcome and Predictors of Survival in Thai Adult Rhabdomyosarcoma Cases.
Sookprasert A, Ungareewittaya P, Manotepitipongse A, Wirasorn K, Chindaprasirt J
Asian Pac J Cancer Prev 2016;17(3):1449-52. doi: 10.7314/apjcp.2016.17.3.1449. PMID: 27039788
Treatment of adult rhabdomyosarcoma.
Ogilvie CM, Crawford EA, Slotcavage RL, King JJ, Lackman RD, Hartner L, Staddon AP
Am J Clin Oncol 2010 Apr;33(2):128-31. doi: 10.1097/COC.0b013e3181979222. PMID: 19770626

Recent clinical studies

Etiology

Adult Pleomorphic Rhabdomyosarcoma: A Multicentre Retrospective Study.
Noujaim J, Thway K, Jones RL, Miah A, Khabra K, Langer R, Kasper B, Judson I, Benson C, Kollàr A
Anticancer Res 2015 Nov;35(11):6213-7. PMID: 26504053

Diagnosis

Molecular characterization of a bladder pleomorphic rhabdomyosarcoma in an adult patient.
Feroce F, Cantile M, Aquino G, Collina F, Scognamiglio G, Castaldo L, Perdonà S, Botti G, De Chiara A
Pathol Res Pract 2020 Aug;216(8):153033. Epub 2020 May 28 doi: 10.1016/j.prp.2020.153033. PMID: 32703497
Adult Pleomorphic Rhabdomyosarcoma: A Multicentre Retrospective Study.
Noujaim J, Thway K, Jones RL, Miah A, Khabra K, Langer R, Kasper B, Judson I, Benson C, Kollàr A
Anticancer Res 2015 Nov;35(11):6213-7. PMID: 26504053
Immunohistochemistry of MyoD1 in adult pleomorphic soft tissue sarcomas.
Wesche WA, Fletcher CD, Dias P, Houghton PJ, Parham DM
Am J Surg Pathol 1995 Mar;19(3):261-9. doi: 10.1097/00000478-199503000-00003. PMID: 7872424

Therapy

Adult Pleomorphic Rhabdomyosarcoma: A Multicentre Retrospective Study.
Noujaim J, Thway K, Jones RL, Miah A, Khabra K, Langer R, Kasper B, Judson I, Benson C, Kollàr A
Anticancer Res 2015 Nov;35(11):6213-7. PMID: 26504053

Prognosis

Molecular characterization of a bladder pleomorphic rhabdomyosarcoma in an adult patient.
Feroce F, Cantile M, Aquino G, Collina F, Scognamiglio G, Castaldo L, Perdonà S, Botti G, De Chiara A
Pathol Res Pract 2020 Aug;216(8):153033. Epub 2020 May 28 doi: 10.1016/j.prp.2020.153033. PMID: 32703497
Adult Pleomorphic Rhabdomyosarcoma: A Multicentre Retrospective Study.
Noujaim J, Thway K, Jones RL, Miah A, Khabra K, Langer R, Kasper B, Judson I, Benson C, Kollàr A
Anticancer Res 2015 Nov;35(11):6213-7. PMID: 26504053

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