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Extra-Adrenal Retroperitoneal Paraganglioma

MedGen UID:
232479
•Concept ID:
C1333495
•
Neoplastic Process
Synonyms: Paraganglioma of Extra-Adrenal Retroperitoneal Area; Paraganglioma of the Extra-Adrenal Retroperitoneal Area

Definition

A sympathetic paraganglioma arising from the retroperitoneum, outside the adrenal gland. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVExtra-Adrenal Retroperitoneal Paraganglioma

Professional guidelines

PubMed

Treatment of metastatic chemodectoma.
Massey V, Wallner K
Cancer 1992 Feb 1;69(3):790-2. doi: 10.1002/1097-0142(19920201)69:3<790::aid-cncr2820690329>3.0.co;2-u. PMID: 1309681
Extraadrenal retroperitoneal paragangliomas: natural history and response to treatment.
Sclafani LM, Woodruff JM, Brennan MF
Surgery 1990 Dec;108(6):1124-9; discussion 1129-30. PMID: 2174194

Recent clinical studies

Etiology

Preoperative Alpha-Blocker Therapy in Patients with Missed Preoperative Diagnosis of Extra-Adrenal Retroperitoneal Paraganglioma Undergoing Resection: A Retrospective Study of 167 Cases at a Single Center.
Liu Y, Jin X, Gao J, Jiang S, Liu L, Lou J, Wang B, Zhang H, Fu Q
Neuroendocrinology 2022;112(5):457-466. Epub 2021 May 31 doi: 10.1159/000517196. PMID: 34004598
Functional extra-adrenal paraganglioma of the retroperitoneum giving thoracolumbar spine metastases after a five-year disease-free follow-up: a rare malignant condition with challenging management.
Kapetanakis S, Chourmouzi D, Gkasdaris G, Katsaridis V, Eleftheriadis E, Givissis P
Pan Afr Med J 2017;28:94. Epub 2017 Sep 29 doi: 10.11604/pamj.2017.28.94.13783. PMID: 29255564Free PMC Article

Diagnosis

Preoperative Alpha-Blocker Therapy in Patients with Missed Preoperative Diagnosis of Extra-Adrenal Retroperitoneal Paraganglioma Undergoing Resection: A Retrospective Study of 167 Cases at a Single Center.
Liu Y, Jin X, Gao J, Jiang S, Liu L, Lou J, Wang B, Zhang H, Fu Q
Neuroendocrinology 2022;112(5):457-466. Epub 2021 May 31 doi: 10.1159/000517196. PMID: 34004598
Functional extra-adrenal paraganglioma of the retroperitoneum giving thoracolumbar spine metastases after a five-year disease-free follow-up: a rare malignant condition with challenging management.
Kapetanakis S, Chourmouzi D, Gkasdaris G, Katsaridis V, Eleftheriadis E, Givissis P
Pan Afr Med J 2017;28:94. Epub 2017 Sep 29 doi: 10.11604/pamj.2017.28.94.13783. PMID: 29255564Free PMC Article
Extra adrenal retroperitoneal paraganglioma.
Bismar HA, Murshid KR
Saudi Med J 2003 Jul;24(7):778-80. PMID: 12883615
Non-functional malignant extra-adrenal retroperitoneal paraganglioma.
Holden A
Australas Radiol 1995 Nov;39(4):392-5. doi: 10.1111/j.1440-1673.1995.tb00319.x. PMID: 8561717
Extra-adrenal retroperitoneal paraganglioma.
Anderson CB, Ward S, Lee J, Rosai J
Am Surg 1974 Nov;40(11):636-42. PMID: 4374105

Prognosis

Functional extra-adrenal paraganglioma of the retroperitoneum giving thoracolumbar spine metastases after a five-year disease-free follow-up: a rare malignant condition with challenging management.
Kapetanakis S, Chourmouzi D, Gkasdaris G, Katsaridis V, Eleftheriadis E, Givissis P
Pan Afr Med J 2017;28:94. Epub 2017 Sep 29 doi: 10.11604/pamj.2017.28.94.13783. PMID: 29255564Free PMC Article

Clinical prediction guides

Malignant paraganglioma of the retroperitoneum with lung metastases: a 13-year survivor after radical surgery.
Matsui H, Ikeuchi S, Onoda N, Tsutsumi Y
Asian J Surg 2007 Jan;30(1):75-9. doi: 10.1016/S1015-9584(09)60133-0. PMID: 17337377

Supplemental Content

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