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Prader-Willi syndrome due to translocation

MedGen UID:
1826085
Concept ID:
C5680509
Disease or Syndrome
Monarch Initiative: MONDO:0015785
Orphanet: ORPHA177907

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPrader-Willi syndrome due to translocation

Professional guidelines

PubMed

Torun D, Akin O
Clin Dysmorphol 2024 Oct 1;33(4):145-151. Epub 2024 Jun 18 doi: 10.1097/MCD.0000000000000506. PMID: 38934057
Schmok T, Surampalli A, Khare M, Zandihaghighi S, Baghbaninogourani R, Patolia B, Gold JA, Naidu A, Cassidy SB, Kimonis VE
Am J Med Genet A 2024 Oct;194(10):e63724. Epub 2024 Jun 4 doi: 10.1002/ajmg.a.63724. PMID: 38837660
Goldstone AP, Holland AJ, Hauffa BP, Hokken-Koelega AC, Tauber M; speakers contributors at the Second Expert Meeting of the Comprehensive Care of Patients with PWS
J Clin Endocrinol Metab 2008 Nov;93(11):4183-97. Epub 2008 Aug 12 doi: 10.1210/jc.2008-0649. PMID: 18697869

Recent clinical studies

Etiology

Schmok T, Surampalli A, Khare M, Zandihaghighi S, Baghbaninogourani R, Patolia B, Gold JA, Naidu A, Cassidy SB, Kimonis VE
Am J Med Genet A 2024 Oct;194(10):e63724. Epub 2024 Jun 4 doi: 10.1002/ajmg.a.63724. PMID: 38837660
Schäffers OJM, Hoenderop JGJ, Bindels RJM, de Baaij JHF
Am J Physiol Renal Physiol 2018 Jun 1;314(6):F1027-F1033. Epub 2018 Feb 7 doi: 10.1152/ajprenal.00634.2017. PMID: 29412701
Dang V, Surampalli A, Manzardo AM, Youn S, Butler MG, Gold JA, Kimonis VE
Cytogenet Genome Res 2016;150(1):29-34. Epub 2016 Nov 29 doi: 10.1159/000452611. PMID: 27894106Free PMC Article
Grugni G, Crinò A, Bedogni G, Cappa M, Sartorio A, Corrias A, Di Candia S, Gargantini L, Iughetti L, Pagano C, Ragusa L, Salvatoni A, Spera S, Vettor R, Chiumello G, Brambilla P
Nutr Metab Cardiovasc Dis 2013 Nov;23(11):1134-40. Epub 2012 Dec 7 doi: 10.1016/j.numecd.2012.11.006. PMID: 23220075
Yamazawa K, Ogata T, Ferguson-Smith AC
Am J Med Genet C Semin Med Genet 2010 Aug 15;154C(3):329-34. doi: 10.1002/ajmg.c.30270. PMID: 20803655

Diagnosis

Salvatore M, Torreri P, Grugni G, Rocchetti A, Maghnie M, Patti G, Crinò A, Elia M, Greco D, Romano C, Franzese A, Mozzillo E, Colao A, Pugliese G, Pagotto U, Lo Preiato V, Scarano E, Schiavariello C, Tornese G, Fintini D, Bocchini S, Osimani S, De Sanctis L, Sacco M, Rutigliano I, Delvecchio M, Faienza MF, Wasniewska M, Corica D, Stagi S, Guazzarotti L, Maffei P, Dassie F, Taruscio D
Orphanet J Rare Dis 2023 Feb 15;18(1):28. doi: 10.1186/s13023-023-02633-5. PMID: 36793093Free PMC Article
Botezatu A, Puiu M, Cucu N, Diaconu CC, Badiu C, Arsene C, Iancu IV, Plesa A, Anton G
Gene 2016 Jan 10;575(2 Pt 1):353-8. Epub 2015 Sep 1 doi: 10.1016/j.gene.2015.08.058. PMID: 26335514
Cassidy SB, Ledbetter DH
Neurol Clin 1989 Feb;7(1):37-54. PMID: 2646521
Pembrey M, Baraitser M
Postgrad Med J 1986 Feb;62(724):131-42. doi: 10.1136/pgmj.62.724.131. PMID: 3540928Free PMC Article
Schneider HJ, Zellweger H
Helv Paediatr Acta 1968 Apr;23(2):128-35. PMID: 4387003

Therapy

Schmok T, Surampalli A, Khare M, Zandihaghighi S, Baghbaninogourani R, Patolia B, Gold JA, Naidu A, Cassidy SB, Kimonis VE
Am J Med Genet A 2024 Oct;194(10):e63724. Epub 2024 Jun 4 doi: 10.1002/ajmg.a.63724. PMID: 38837660
Botezatu A, Puiu M, Cucu N, Diaconu CC, Badiu C, Arsene C, Iancu IV, Plesa A, Anton G
Gene 2016 Jan 10;575(2 Pt 1):353-8. Epub 2015 Sep 1 doi: 10.1016/j.gene.2015.08.058. PMID: 26335514
Grugni G, Crinò A, Bosio L, Corrias A, Cuttini M, De Toni T, Di Battista E, Franzese A, Gargantini L, Greggio N, Iughetti L, Livieri C, Naselli A, Pagano C, Pozzan G, Ragusa L, Salvatoni A, Trifirò G, Beccaria L, Bellizzi M, Bellone J, Brunani A, Cappa M, Caselli G, Cerioni V, Delvecchio M, Giardino D, Iannì F, Memo L, Pilotta A, Pomara C, Radetti G, Sacco M, Sanzari A, Sartorio A, Tonini G, Vettor R, Zaglia F, Chiumello G; Genetic Obesity Study Group of Italian Society of Pediatric Endocrinology and Diabetology (ISPED)
Am J Med Genet A 2008 Apr 1;146A(7):861-72. doi: 10.1002/ajmg.a.32133. PMID: 18203198
Ann Genet 1989;32(1):5-9. PMID: 2665630
Therman E, Susman B, Denniston C
Ann Hum Genet 1989 Jan;53(1):49-65. doi: 10.1111/j.1469-1809.1989.tb01121.x. PMID: 2658738

Prognosis

Rafi SK, Butler MG
Int J Mol Sci 2020 May 6;21(9) doi: 10.3390/ijms21093296. PMID: 32384786Free PMC Article
Xefteris A, Sekerli E, Arampatzi A, Charisiou S, Oikonomidou E, Efstathiou G, Peroulis N, Malamidou A, Tsoulou-Panidou E, Agakidou E, Sarafidis K, Psarakis A, Kataras T, Daskalakis G
Cytogenet Genome Res 2019;159(3):109-118. Epub 2019 Dec 10 doi: 10.1159/000504159. PMID: 31816617
Harada-Shirado K, Ikeda K, Matsumoto H, Shiga Y, Furukawa M, Takahashi H, Ohkawara H, Noji H, Hashimoto Y, Waguri S, Watanabe S, Ogawa K, Takeishi Y
Clin Lymphoma Myeloma Leuk 2014 Apr;14(2):e69-72. Epub 2013 Nov 15 doi: 10.1016/j.clml.2013.10.009. PMID: 24361186
Liu AP, Tang WF, Lau ET, Chan KY, Kan AS, Wong KY, Tso WW, Jalal K, Lee SL, Chau CS, Chung BH
Am J Med Genet A 2013 Jun;161A(6):1309-18. Epub 2013 Apr 30 doi: 10.1002/ajmg.a.35909. PMID: 23633107
Phelan MC
Orphanet J Rare Dis 2008 May 27;3:14. doi: 10.1186/1750-1172-3-14. PMID: 18505557Free PMC Article

Clinical prediction guides

Torun D, Akin O
Clin Dysmorphol 2024 Oct 1;33(4):145-151. Epub 2024 Jun 18 doi: 10.1097/MCD.0000000000000506. PMID: 38934057
Castilla-Vallmanya L, Centeno-Pla M, Serrano M, Franco-Valls H, Martínez-Cabrera R, Prat-Planas A, Rojano E, Ranea JAG, Seoane P, Oliva C, Paredes-Fuentes AJ, Marfany G, Artuch R, Grinberg D, Rabionet R, Balcells S, Urreizti R
J Med Genet 2023 Apr;60(4):406-415. Epub 2022 Sep 7 doi: 10.1136/jmg-2022-108690. PMID: 36243518Free PMC Article
Eisfeldt J, Rezayee F, Pettersson M, Lagerstedt K, Malmgren H, Falk A, Grigelioniene G, Lindstrand A
Hum Mutat 2022 Nov;43(11):1567-1575. Epub 2022 Jul 23 doi: 10.1002/humu.24440. PMID: 35842787Free PMC Article
Grugni G, Crinò A, Bedogni G, Cappa M, Sartorio A, Corrias A, Di Candia S, Gargantini L, Iughetti L, Pagano C, Ragusa L, Salvatoni A, Spera S, Vettor R, Chiumello G, Brambilla P
Nutr Metab Cardiovasc Dis 2013 Nov;23(11):1134-40. Epub 2012 Dec 7 doi: 10.1016/j.numecd.2012.11.006. PMID: 23220075
Emanuel BS, Shaikh TH
Nat Rev Genet 2001 Oct;2(10):791-800. doi: 10.1038/35093500. PMID: 11584295

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