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Recurrent Clear Cell Sarcoma of Soft Tissue

MedGen UID:
1793208
•Concept ID:
C5556767
•
Neoplastic Process

Definition

The reemergence of clear cell sarcoma of soft tissue after a period of remission. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRecurrent Clear Cell Sarcoma of Soft Tissue

Professional guidelines

PubMed

Clear cell chondrosarcoma: a review of clinicopathologic characteristics, differential diagnoses, and patient management.
Alexiev BA, Vormittag-Nocito ER, Peabody TD, Samet J, Laskin WB
Hum Pathol 2023 Sep;139:126-134. Epub 2023 Jun 16 doi: 10.1016/j.humpath.2023.06.004. PMID: 37805864
Management of the Hand Tumors.
Datta NK, Das KP, Aish PK, Datta M, Banik SK, Sen SK, Chowdhury RM
Mymensingh Med J 2023 Jan;32(1):135-143. PMID: 36594313
Wilms' tumor management.
Wu HY, Snyder HM 3rd, D'Angio GJ
Curr Opin Urol 2005 Jul;15(4):273-6. doi: 10.1097/01.mou.0000172403.69890.eb. PMID: 15928519

Recent clinical studies

Etiology

Cutaneous Melanocytic Tumor With CRTC1::TRIM11 Translocation : An Emerging Entity Analyzed in a Series of 41 Cases.
Hanna J, Ko JS, Billings SD, Boivin F, Beaudoux O, Pissaloux D, Tirode F, Laga A, Fletcher CDM, de la Fouchardiere A
Am J Surg Pathol 2022 Nov 1;46(11):1457-1466. Epub 2022 Aug 23 doi: 10.1097/PAS.0000000000001952. PMID: 35993578
Overexpression of BMP1 reflects poor prognosis in clear cell renal cell carcinoma.
Xiao W, Wang X, Wang T, Xing J
Cancer Gene Ther 2020 May;27(5):330-340. Epub 2019 Jun 3 doi: 10.1038/s41417-019-0107-9. PMID: 31155610Free PMC Article
Dermatofibrosarcoma Protuberans.
Allen A, Ahn C, Sangüeza OP
Dermatol Clin 2019 Oct;37(4):483-488. doi: 10.1016/j.det.2019.05.006. PMID: 31466588
Clear cell chondrosarcoma of the larynx.
Hendriks T, Cardemil F, Sader C
BMJ Case Rep 2018 Sep 4;2018 doi: 10.1136/bcr-2018-226541. PMID: 30181407Free PMC Article
Wilms' tumor management.
Wu HY, Snyder HM 3rd, D'Angio GJ
Curr Opin Urol 2005 Jul;15(4):273-6. doi: 10.1097/01.mou.0000172403.69890.eb. PMID: 15928519

Diagnosis

Clear cell chondrosarcoma: a review of clinicopathologic characteristics, differential diagnoses, and patient management.
Alexiev BA, Vormittag-Nocito ER, Peabody TD, Samet J, Laskin WB
Hum Pathol 2023 Sep;139:126-134. Epub 2023 Jun 16 doi: 10.1016/j.humpath.2023.06.004. PMID: 37805864
The many faces of Atypical fibroxanthoma.
Agaimy A
Semin Diagn Pathol 2023 Jul;40(4):306-312. Epub 2023 Jun 23 doi: 10.1053/j.semdp.2023.06.001. PMID: 37438163
Options for treating different soft tissue sarcoma subtypes.
Ray-Coquard I, Serre D, Reichardt P, Martín-Broto J, Bauer S
Future Oncol 2018 May;14(10s):25-49. doi: 10.2217/fon-2018-0076. PMID: 29768052
Wilms' tumor management.
Wu HY, Snyder HM 3rd, D'Angio GJ
Curr Opin Urol 2005 Jul;15(4):273-6. doi: 10.1097/01.mou.0000172403.69890.eb. PMID: 15928519
Soft tissue sarcoma of the upper extremity.
Murray PM
Hand Clin 2004 Aug;20(3):325-33, vii. doi: 10.1016/j.hcl.2004.03.007. PMID: 15275691

Therapy

Translating Knowledge About the Immune Microenvironment of Gastrointestinal Stromal Tumors into Effective Clinical Strategies.
Chantharasamee J, Adashek JJ, Wong K, Eckardt MA, Chmielowski B, Dry S, Eilber FC, Singh AS
Curr Treat Options Oncol 2021 Jan 5;22(1):9. doi: 10.1007/s11864-020-00806-z. PMID: 33400014
BCOR-CCNB3 fusion-positive clear cell sarcoma of the kidney.
Han H, Bertrand KC, Patel KR, Fisher KE, Roy A, Muscal JA, Venkatramani R
Pediatr Blood Cancer 2020 Apr;67(4):e28151. Epub 2019 Dec 26 doi: 10.1002/pbc.28151. PMID: 31876361
Dermatofibrosarcoma Protuberans.
Allen A, Ahn C, Sangüeza OP
Dermatol Clin 2019 Oct;37(4):483-488. doi: 10.1016/j.det.2019.05.006. PMID: 31466588
Options for treating different soft tissue sarcoma subtypes.
Ray-Coquard I, Serre D, Reichardt P, Martín-Broto J, Bauer S
Future Oncol 2018 May;14(10s):25-49. doi: 10.2217/fon-2018-0076. PMID: 29768052
Wilms' tumor management.
Wu HY, Snyder HM 3rd, D'Angio GJ
Curr Opin Urol 2005 Jul;15(4):273-6. doi: 10.1097/01.mou.0000172403.69890.eb. PMID: 15928519

Prognosis

Cutaneous Melanocytic Tumor With CRTC1::TRIM11 Translocation : An Emerging Entity Analyzed in a Series of 41 Cases.
Hanna J, Ko JS, Billings SD, Boivin F, Beaudoux O, Pissaloux D, Tirode F, Laga A, Fletcher CDM, de la Fouchardiere A
Am J Surg Pathol 2022 Nov 1;46(11):1457-1466. Epub 2022 Aug 23 doi: 10.1097/PAS.0000000000001952. PMID: 35993578
Options for treating different soft tissue sarcoma subtypes.
Ray-Coquard I, Serre D, Reichardt P, Martín-Broto J, Bauer S
Future Oncol 2018 May;14(10s):25-49. doi: 10.2217/fon-2018-0076. PMID: 29768052
Clear cell sarcoma of soft tissues.
Malchau SS, Hayden J, Hornicek F, Mankin HJ
J Surg Oncol 2007 May 1;95(6):519-22. doi: 10.1002/jso.20730. PMID: 17192915
Wilms' tumor management.
Wu HY, Snyder HM 3rd, D'Angio GJ
Curr Opin Urol 2005 Jul;15(4):273-6. doi: 10.1097/01.mou.0000172403.69890.eb. PMID: 15928519
Soft tissue sarcoma of the upper extremity.
Murray PM
Hand Clin 2004 Aug;20(3):325-33, vii. doi: 10.1016/j.hcl.2004.03.007. PMID: 15275691

Clinical prediction guides

STAG2 loss rewires oncogenic and developmental programs to promote metastasis in Ewing sarcoma.
Adane B, Alexe G, Seong BKA, Lu D, Hwang EE, Hnisz D, Lareau CA, Ross L, Lin S, Dela Cruz FS, Richardson M, Weintraub AS, Wang S, Iniguez AB, Dharia NV, Conway AS, Robichaud AL, Tanenbaum B, Krill-Burger JM, Vazquez F, Schenone M, Berman JN, Kung AL, Carr SA, Aryee MJ, Young RA, Crompton BD, Stegmaier K
Cancer Cell 2021 Jun 14;39(6):827-844.e10. doi: 10.1016/j.ccell.2021.05.007. PMID: 34129824Free PMC Article
Atypical fibroxanthoma and pleomorphic dermal sarcoma: A reappraisal.
Cesinaro AM, Gallo G, Tramontozzi S, Migaldi M
J Cutan Pathol 2021 Feb;48(2):207-210. Epub 2020 Jul 28 doi: 10.1111/cup.13787. PMID: 32583897
Overexpression of BMP1 reflects poor prognosis in clear cell renal cell carcinoma.
Xiao W, Wang X, Wang T, Xing J
Cancer Gene Ther 2020 May;27(5):330-340. Epub 2019 Jun 3 doi: 10.1038/s41417-019-0107-9. PMID: 31155610Free PMC Article
Clear cell sarcoma of the kidney in a child with Fanconi anemia.
Trejo Bittar HE, Radder JE, Ranganathan S, Srinivasan A, Madan-Khetarpal S, Reyes-Múgica M
Pediatr Dev Pathol 2014 Jul-Aug;17(4):297-301. Epub 2014 Apr 15 doi: 10.2350/14-03-1450-CR.1. PMID: 24735155
Diagnosis, classification, and management of soft tissue sarcomas.
Mankin HJ, Hornicek FJ
Cancer Control 2005 Jan-Feb;12(1):5-21. doi: 10.1177/107327480501200102. PMID: 15668648

Recent systematic reviews

Primary pulmonary hyalinizing clear cell carcinoma with vocal-cord squamous cell carcinoma: a case report with systematic review.
Li Z, Li W, Xue L
Diagn Pathol 2023 Aug 8;18(1):90. doi: 10.1186/s13000-023-01376-y. PMID: 37553667Free PMC Article
Clinicopathological Features Associated with Microsatellite Instability/Mismatch Repair Deficiency in Uterine Carcinosarcoma: A Quantitative Systematic Review.
Travaglino A, Raffone A, Santoro A, Raimondo D, Orsini B, Casadio P, Zullo F, Seracchioli R, Zannoni GF, Insabato L, Mollo A
Pathobiology 2022;89(4):198-204. Epub 2022 Mar 1 doi: 10.1159/000521876. PMID: 35231921

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