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Kidney Epithelioid Angiomyolipoma

MedGen UID:
1677196
Concept ID:
C4763994
Neoplastic Process
Synonyms: Epithelioid Angiomyolipoma/Epithelioid PEComa of the Kidney; Kidney EAML; Kidney Epithelioid Type Angiomyolipoma; Perivascular Epithelioid Cell Tumor of the Kidney; Renal Epithelioid Angiomyolipoma

Definition

An angiomyolipoma that arises from the kidney and is composed exclusively or predominantly of epithelioid cells. It is often associated with cytologic atypia and may recur or metastasize. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVKidney Epithelioid Angiomyolipoma

Professional guidelines

PubMed

Yang JW, Liang C, Yang L
Kaohsiung J Med Sci 2022 Oct;38(10):925-932. Epub 2022 Sep 3 doi: 10.1002/kjm2.12586. PMID: 36056704
Jinzaki M, Silverman SG, Akita H, Nagashima Y, Mikami S, Oya M
Abdom Imaging 2014 Jun;39(3):588-604. doi: 10.1007/s00261-014-0083-3. PMID: 24504542Free PMC Article
Nelson CP, Sanda MG
J Urol 2002 Oct;168(4 Pt 1):1315-25. doi: 10.1016/S0022-5347(05)64440-0. PMID: 12352384

Recent clinical studies

Etiology

Caliò A, Brunelli M, Marletta S, Zamboni G, Bonetti F, Pea M, Martignoni G
Pathologica 2021 Oct;113(5):307-315. doi: 10.32074/1591-951X-335. PMID: 34837089Free PMC Article
Çalışkan S, Gümrükçü G, Özsoy E, Topaktas R, Öztürk Mİ
Rev Assoc Med Bras (1992) 2019 Aug 5;65(7):977-981. doi: 10.1590/1806-9282.65.7.977. PMID: 31389508
Martignoni G, Pea M, Zampini C, Brunelli M, Segala D, Zamboni G, Bonetti F
Semin Diagn Pathol 2015 Mar;32(2):140-59. Epub 2015 Feb 24 doi: 10.1053/j.semdp.2015.02.006. PMID: 25804448
Vicens RA, Jensen CT, Korivi BR, Bhosale PR
J Comput Assist Tomogr 2014 Jul-Aug;38(4):574-7. doi: 10.1097/RCT.0000000000000101. PMID: 24887578
Haas NB, Nathanson KL
Adv Chronic Kidney Dis 2014 Jan;21(1):81-90. doi: 10.1053/j.ackd.2013.10.001. PMID: 24359990Free PMC Article

Diagnosis

Salles DC, Asrani K, Woo J, Vidotto T, Liu HB, Vidal I, Matoso A, Netto GJ, Argani P, Lotan TL
J Pathol 2022 Jun;257(2):158-171. Epub 2022 Mar 29 doi: 10.1002/path.5875. PMID: 35072947Free PMC Article
Caliò A, Brunelli M, Marletta S, Zamboni G, Bonetti F, Pea M, Martignoni G
Pathologica 2021 Oct;113(5):307-315. doi: 10.32074/1591-951X-335. PMID: 34837089Free PMC Article
Erickson LA
Mayo Clin Proc 2020 Jan;95(1):205-206. doi: 10.1016/j.mayocp.2019.11.015. PMID: 31902422
Çalışkan S, Gümrükçü G, Özsoy E, Topaktas R, Öztürk Mİ
Rev Assoc Med Bras (1992) 2019 Aug 5;65(7):977-981. doi: 10.1590/1806-9282.65.7.977. PMID: 31389508
Goodman ZD, Ishak KG
Am J Surg Pathol 1984 Oct;8(10):745-50. doi: 10.1097/00000478-198410000-00003. PMID: 6496843

Therapy

Hatano T, Egawa S
Asian J Surg 2020 Oct;43(10):967-972. Epub 2020 Jan 17 doi: 10.1016/j.asjsur.2019.12.008. PMID: 31959574
Wang T, Xie S, Luo R, Shi L, Bai P, Wang X, Wan R, Deng J, Wu Z, Li W, Xiao W, Wang Y, Chen B, Zhang K, Xing J
Cancer Biol Ther 2020;21(1):4-11. Epub 2019 Oct 10 doi: 10.1080/15384047.2019.1665955. PMID: 31597506Free PMC Article
Vicens RA, Jensen CT, Korivi BR, Bhosale PR
J Comput Assist Tomogr 2014 Jul-Aug;38(4):574-7. doi: 10.1097/RCT.0000000000000101. PMID: 24887578
Faria E, Turturro F, Rao P, Matin SF
Clin Genitourin Cancer 2013 Dec;11(4):e1-5. Epub 2013 Jun 20 doi: 10.1016/j.clgc.2013.04.032. PMID: 23791549Free PMC Article
Wolff N, Kabbani W, Bradley T, Raj G, Watumull L, Brugarolas J
J Clin Oncol 2010 Feb 10;28(5):e65-8. Epub 2010 Jan 4 doi: 10.1200/JCO.2009.26.3061. PMID: 20048172

Prognosis

Luo C, Liu Z, Gao M, Hu Q, He X, Xi Y, Cai F, Zhang R, Zeng X, Xiao N
Abdom Radiol (NY) 2022 Jan;47(1):310-319. Epub 2021 Oct 19 doi: 10.1007/s00261-021-03313-3. PMID: 34664098
Vicens RA, Jensen CT, Korivi BR, Bhosale PR
J Comput Assist Tomogr 2014 Jul-Aug;38(4):574-7. doi: 10.1097/RCT.0000000000000101. PMID: 24887578
Chen J, Wang P, Wang CJ, Cai SL, Ren GP, Li YY
Chin Med J (Engl) 2010 Mar 20;123(6):765-6. PMID: 20368102
Takahashi N, Kitahara R, Hishimoto Y, Ohguro A, Hashimoto Y, Suzuki T
Int J Urol 2003 May;10(5):271-3. doi: 10.1046/j.1442-2042.2003.00620.x. PMID: 12694468
Eble JN
Semin Diagn Pathol 1998 Feb;15(1):21-40. PMID: 9503504

Clinical prediction guides

Hao YW, Zhang Y, Guo HP, Xu W, Bai X, Zhao J, Ding XH, Gao S, Cui MQ, Liu BC, Ye HY, Wang HY
Abdom Radiol (NY) 2023 Dec;48(12):3714-3727. Epub 2023 Sep 25 doi: 10.1007/s00261-023-04034-5. PMID: 37747536
Salles DC, Asrani K, Woo J, Vidotto T, Liu HB, Vidal I, Matoso A, Netto GJ, Argani P, Lotan TL
J Pathol 2022 Jun;257(2):158-171. Epub 2022 Mar 29 doi: 10.1002/path.5875. PMID: 35072947Free PMC Article
Luo C, Liu Z, Gao M, Hu Q, He X, Xi Y, Cai F, Zhang R, Zeng X, Xiao N
Abdom Radiol (NY) 2022 Jan;47(1):310-319. Epub 2021 Oct 19 doi: 10.1007/s00261-021-03313-3. PMID: 34664098
Schieda N, Kielar AZ, Al Dandan O, McInnes MD, Flood TA
Clin Radiol 2015 Feb;70(2):206-20. Epub 2014 Nov 15 doi: 10.1016/j.crad.2014.10.001. PMID: 25468637
Dickson BC, Brooks JS, Pasha TL, Zhang PJ
Int J Surg Pathol 2011 Feb;19(1):26-30. Epub 2010 Feb 16 doi: 10.1177/1066896909352861. PMID: 20164056

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