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15q overgrowth syndrome

MedGen UID:
1661769
Concept ID:
C4749920
Disease or Syndrome
Synonym: 15q26 overgrowth syndrome
SNOMED CT: 15q overgrowth syndrome (771477003)
Modes of inheritance:
Unknown inheritance
MedGen UID:
989040
Concept ID:
CN307042
Finding
Source: Orphanet
Hereditary clinical entity whose mode of inheritance is unknown.
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Monarch Initiative: MONDO:0017806
Orphanet: ORPHA314585

Definition

A rare partial autosomal trisomy/tetrasomy characterised by facial dysmorphism (long thin face, prominent forehead, down-slanting palpebral fissures, prominent nose with broad nasal bridge, prominent chin), pre and postnatal overgrowth, renal anomalies (for example horseshoe kidney, renal agenesis, hydronephrosis), mild to severe learning difficulties and behavioural abnormalities. Additional features may include craniosynostosis and macrocephaly. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGV15q overgrowth syndrome

Recent clinical studies

Etiology

Bodle EE, Gupta R, Cherry AM, Muffly L, Manning MA
Am J Med Genet A 2019 Jun;179(6):1025-1029. Epub 2019 Mar 12 doi: 10.1002/ajmg.a.61115. PMID: 30861314

Diagnosis

Bodle EE, Gupta R, Cherry AM, Muffly L, Manning MA
Am J Med Genet A 2019 Jun;179(6):1025-1029. Epub 2019 Mar 12 doi: 10.1002/ajmg.a.61115. PMID: 30861314
Chen CP, Lin YH, Au HK, Su YN, Hsu CY, Liu YP, Wu PC, Chern SR, Chen YT, Chen LF, Hsieh AH, Wang W
Taiwan J Obstet Gynecol 2011 Sep;50(3):359-65. doi: 10.1016/j.tjog.2011.07.004. PMID: 22030053
Gutiérrez-Franco Mde L, Madariaga-Campos Mde L, Vásquez-Velásquez AI, Matute E, Guevara-Yáñez R, Rivera H
Korean J Lab Med 2010 Jun;30(3):318-24. doi: 10.3343/kjlm.2010.30.3.318. PMID: 20603595

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