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Hypoplastic right atrium

MedGen UID:
1624318
Concept ID:
C4531222
Congenital Abnormality
HPO: HP:0031294

Definition

Underdeveloped, small right heart atrium. [from HPO]

Term Hierarchy

Professional guidelines

PubMed

Peng R, Xie HN, Zhu YX, Li LJ, Du L, Zheng J
J Ultrasound Med 2014 Jul;33(7):1155-61. doi: 10.7863/ultra.33.7.1155. PMID: 24958401
Glatz JA, Tabbutt S, Gaynor JW, Rome JJ, Montenegro L, Spray TL, Rychik J
Ann Thorac Surg 2007 Nov;84(5):1633-8. doi: 10.1016/j.athoracsur.2007.06.061. PMID: 17954074
Bacha EA, Kreutzer J
J Interv Cardiol 2001 Jun;14(3):367-75. doi: 10.1111/j.1540-8183.2001.tb00346.x. PMID: 12053398

Recent clinical studies

Etiology

Johnson BA, Shepherd J, Bhombal S, Ali N, Joynt C
Semin Perinatol 2024 Dec;48(8):151989. Epub 2024 Oct 8 doi: 10.1016/j.semperi.2024.151989. PMID: 39477714
Sanchez-Escobar IC, Giraldo-Pinto M, Quintero-Gomez A, Arias A, de la Peña A, García R, Gutierrez J, Uribe A, Lince-Varela R, Ruz Montes M, Espinal JA, Correa-Velasquez R
World J Pediatr Congenit Heart Surg 2024 Mar;15(2):226-230. Epub 2023 Nov 21 doi: 10.1177/21501351231196484. PMID: 37990527
Rentschler S, Harris BS, Kuznekoff L, Jain R, Manderfield L, Lu MM, Morley GE, Patel VV, Epstein JA
J Clin Invest 2011 Feb;121(2):525-33. Epub 2011 Jan 25 doi: 10.1172/JCI44470. PMID: 21266778Free PMC Article
Lim DS, Peeler BB, Matherne GP, Kron IL, Gutgesell HP
Pediatr Cardiol 2006 Jan-Feb;27(1):91-95. doi: 10.1007/s00246-005-1028-y. PMID: 16132295
Bacha EA, Kreutzer J
J Interv Cardiol 2001 Jun;14(3):367-75. doi: 10.1111/j.1540-8183.2001.tb00346.x. PMID: 12053398

Diagnosis

Sanchez-Escobar IC, Giraldo-Pinto M, Quintero-Gomez A, Arias A, de la Peña A, García R, Gutierrez J, Uribe A, Lince-Varela R, Ruz Montes M, Espinal JA, Correa-Velasquez R
World J Pediatr Congenit Heart Surg 2024 Mar;15(2):226-230. Epub 2023 Nov 21 doi: 10.1177/21501351231196484. PMID: 37990527
Chen PF, Peng R, Tang L, Hu XQ
Eur Heart J Cardiovasc Imaging 2018 May 1;19(5):583. doi: 10.1093/ehjci/jex320. PMID: 29444259
Suzuki S, Kise H, Kaga S, Hoshiai M, Koizumi K, Hasebe Y, Motohashi S, Matsumoto M
Gen Thorac Cardiovasc Surg 2015 Aug;63(8):472-5. Epub 2013 Aug 3 doi: 10.1007/s11748-013-0304-7. PMID: 23907363
Thankavel PP, Gabbert B, Ramaciotti C
Echocardiography 2014 May;31(5):E163-5. Epub 2014 Mar 25 doi: 10.1111/echo.12565. PMID: 24660671
Bardo DM, Frankel DG, Applegate KE, Murphy DJ, Saneto RP
Radiographics 2001 May-Jun;21(3):705-17. doi: 10.1148/radiographics.21.3.g01ma09705. PMID: 11353117

Therapy

António M, Gordo A, Pereira C, Pinto F, Fragata I, Fragata J
Ann Thorac Surg 2016 Jun;101(6):2370-3. doi: 10.1016/j.athoracsur.2015.08.079. PMID: 27211948
O'Connor MJ, Imamura M, Dyamenahalli U
Circulation 2013 Sep 24;128(13):e193-4. doi: 10.1161/CIRCULATIONAHA.113.001595. PMID: 24060946
Bielefeld KJ, Seib PM, Fontenot EE
Catheter Cardiovasc Interv 2012 Nov 15;80(6):940-3. Epub 2012 Nov 8 doi: 10.1002/ccd.24400. PMID: 22517585
Nemeh HW, Reddy S, Walters HL 3rd, Hakimi M, Ross RD
Ann Thorac Surg 2003 Dec;76(6):2089-91. doi: 10.1016/s0003-4975(03)01173-1. PMID: 14667654
Kuhn MA, Larsen RL, Mulla NF, Johnston JK, Chinnock RE, Bailey LL
Am J Cardiol 2000 Jan 1;85(1):124-7, A9. doi: 10.1016/s0002-9149(99)00624-4. PMID: 11078255

Prognosis

Bo I, Carvalho JS, Cheasty E, Rubens M, Rigby ML
Cardiol Young 2016 Jun;26(5):941-7. Epub 2015 Sep 16 doi: 10.1017/S1047951115001651. PMID: 26374351
Suzuki S, Kise H, Kaga S, Hoshiai M, Koizumi K, Hasebe Y, Motohashi S, Matsumoto M
Gen Thorac Cardiovasc Surg 2015 Aug;63(8):472-5. Epub 2013 Aug 3 doi: 10.1007/s11748-013-0304-7. PMID: 23907363
Lim DS, Peeler BB, Matherne GP, Kron IL, Gutgesell HP
Pediatr Cardiol 2006 Jan-Feb;27(1):91-95. doi: 10.1007/s00246-005-1028-y. PMID: 16132295
Kuhn MA, Larsen RL, Mulla NF, Johnston JK, Chinnock RE, Bailey LL
Am J Cardiol 2000 Jan 1;85(1):124-7, A9. doi: 10.1016/s0002-9149(99)00624-4. PMID: 11078255
Norwood WI, Lang P, Hansen DD
N Engl J Med 1983 Jan 6;308(1):23-6. doi: 10.1056/NEJM198301063080106. PMID: 6847920

Clinical prediction guides

Sevgin B, Coban MN, Karatas F, Pekkan K
J Vis Exp 2023 Jun 16;(196) doi: 10.3791/65330. PMID: 37395593
Ito T, Aoki M, Hagino I, Koshiyama H
Gen Thorac Cardiovasc Surg 2023 Jul;71(7):391-395. Epub 2023 Jan 3 doi: 10.1007/s11748-022-01897-1. PMID: 36595159
He D, Sinha P, Jonas RA
J Card Surg 2012 Nov;27(6):758-9. Epub 2012 Oct 19 doi: 10.1111/jocs.12023. PMID: 23078626
Sharma J, Friedman D, Schiller M, Flynn P, Alonso ML
Int J Cardiol 1997 Dec 19;62(3):199-202. doi: 10.1016/s0167-5273(97)00255-6. PMID: 9476678
Kinare SG, Sivaraman A, Deshpande J
Indian Heart J 1989 Sep-Oct;41(5):301-6. PMID: 2599539

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