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Abnormal pulmonary artery morphology

MedGen UID:
1379288
•Concept ID:
C4476881
•
Anatomical Abnormality
HPO: HP:0030966

Definition

An abnormality of the structure of the pulmonary artery. [from HPO]

Professional guidelines

PubMed

Diagnosis and endovascular management of pulmonary arteriovenous malformations.
Kramdhari H, Valakkada J, Ayyappan A
Br J Radiol 2021 Jul 1;94(1123):20200695. Epub 2021 May 26 doi: 10.1259/bjr.20200695. PMID: 34038182Free PMC Article
Primary-care management of patients with congenital anomalies of the coronary arteries.
Boris JR, Brothers JA
Cardiol Young 2015 Dec;25(8):1540-5. doi: 10.1017/S1047951115002127. PMID: 26675602
Primary pulmonary hypertension.
Gaine SP, Rubin LJ
Lancet 1998 Aug 29;352(9129):719-25. doi: 10.1016/S0140-6736(98)02111-4. PMID: 9729004

Recent clinical studies

Etiology

Pulmonary artery sling: An overview.
K Rahmath MR, Durward A
Pediatr Pulmonol 2023 May;58(5):1299-1309. Epub 2023 Feb 24 doi: 10.1002/ppul.26345. PMID: 36790334
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Internal mammary artery-to-pulmonary vasculature fistula: Systematic review of case reports.
Abdul Jabbar A, Patel A, Marzlin N, Altabaqchali S, Hasan M, Al-Zubaidi M, Agarwal A
Vasc Med 2017 Oct;22(5):426-431. doi: 10.1177/1358863X17724262. PMID: 28990495
Discontinuous Pulmonary Artery.
Eltayeb O, Mongé MC, Popescu AR, Sarwark AE, Harris T, Backer CL
World J Pediatr Congenit Heart Surg 2017 Jan;8(1):106-110. Epub 2016 Jun 22 doi: 10.1177/2150135115618871. PMID: 26993757

Diagnosis

Pulmonary artery sling: An overview.
K Rahmath MR, Durward A
Pediatr Pulmonol 2023 May;58(5):1299-1309. Epub 2023 Feb 24 doi: 10.1002/ppul.26345. PMID: 36790334
State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Discontinuous Pulmonary Artery.
Eltayeb O, Mongé MC, Popescu AR, Sarwark AE, Harris T, Backer CL
World J Pediatr Congenit Heart Surg 2017 Jan;8(1):106-110. Epub 2016 Jun 22 doi: 10.1177/2150135115618871. PMID: 26993757
Rings and slings revisited.
Smith BM, Lu JC, Dorfman AL, Mahani MG, Agarwal PP
Magn Reson Imaging Clin N Am 2015 Feb;23(1):127-35. Epub 2014 Oct 3 doi: 10.1016/j.mric.2014.09.011. PMID: 25476681
Coronary-pulmonary artery fistula in tetralogy of Fallot with pulmonary atresia.
Talwar S, Anderson RH, Keshri VK, Choudhary SK, Gulati GS, Airan B
Asian Cardiovasc Thorac Ann 2014 Oct;22(8):1003-9. Epub 2013 Nov 12 doi: 10.1177/0218492313505101. PMID: 24887892

Therapy

The Secrets of the Frogs Heart.
Corno AF, Zhou Z, Uppu SC, Huang S, Marino B, Milewicz DM, Salazar JD
Pediatr Cardiol 2022 Oct;43(7):1471-1480. Epub 2022 Mar 15 doi: 10.1007/s00246-022-02870-8. PMID: 35290490
Tracheoplasty for Patients with Pulmonary Artery Sling and Tracheal Stenosis: A Meta-Analysis.
Li D, Zhou X, Li M
Pediatr Cardiol 2020 Oct;41(7):1376-1385. Epub 2020 Jun 3 doi: 10.1007/s00246-020-02386-z. PMID: 32494877
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Thompson SA, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2015 Jan 29;1:CD008017. doi: 10.1002/14651858.CD008017.pub4. PMID: 25634560

Prognosis

Congenital central pulmonary artery anomalies: Part 2.
Newman B, Alkhori N
Pediatr Radiol 2020 Jul;50(8):1030-1040. Epub 2020 Jun 4 doi: 10.1007/s00247-020-04703-3. PMID: 32500159
Congenital central pulmonary artery anomalies: Part 1.
Newman B, Alkhori N
Pediatr Radiol 2020 Jul;50(8):1022-1029. Epub 2020 May 30 doi: 10.1007/s00247-020-04690-5. PMID: 32474775
State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Coronary-pulmonary artery fistula in tetralogy of Fallot with pulmonary atresia.
Talwar S, Anderson RH, Keshri VK, Choudhary SK, Gulati GS, Airan B
Asian Cardiovasc Thorac Ann 2014 Oct;22(8):1003-9. Epub 2013 Nov 12 doi: 10.1177/0218492313505101. PMID: 24887892
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954

Clinical prediction guides

State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Thompson SA, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2015 Jan 29;1:CD008017. doi: 10.1002/14651858.CD008017.pub4. PMID: 25634560
Coronary-pulmonary artery fistula in tetralogy of Fallot with pulmonary atresia.
Talwar S, Anderson RH, Keshri VK, Choudhary SK, Gulati GS, Airan B
Asian Cardiovasc Thorac Ann 2014 Oct;22(8):1003-9. Epub 2013 Nov 12 doi: 10.1177/0218492313505101. PMID: 24887892
Normal and abnormal pulmonary arteriovenous shunting: occurrence and mechanisms.
Hoffman JI
Cardiol Young 2013 Oct;23(5):629-41. Epub 2013 Mar 5 doi: 10.1017/S1047951113000140. PMID: 23458130

Recent systematic reviews

Pulmonary hypertension secondary to congenital diaphragmatic hernia: factors and pathways involved in pulmonary vascular remodeling.
Montalva L, Antounians L, Zani A
Pediatr Res 2019 May;85(6):754-768. Epub 2019 Feb 19 doi: 10.1038/s41390-019-0345-4. PMID: 30780153
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Internal mammary artery-to-pulmonary vasculature fistula: Systematic review of case reports.
Abdul Jabbar A, Patel A, Marzlin N, Altabaqchali S, Hasan M, Al-Zubaidi M, Agarwal A
Vasc Med 2017 Oct;22(5):426-431. doi: 10.1177/1358863X17724262. PMID: 28990495
Coronary-Pulmonary Artery Fistulas: A Systematic Review.
Verdini D, Vargas D, Kuo A, Ghoshhajra B, Kim P, Murillo H, Kirsch J, Lane M, Restrepo C
J Thorac Imaging 2016 Nov;31(6):380-390. doi: 10.1097/RTI.0000000000000232. PMID: 27768631
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Thompson SA, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2015 Jan 29;1:CD008017. doi: 10.1002/14651858.CD008017.pub4. PMID: 25634560

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