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GTR Home > Conditions/Phenotypes > Wilms tumor 6

Summary

Wilms tumor is the most common renal tumor of childhood, occurring with an incidence of 1 in 10,000. It is often described as an embryonal tumor, as it arises from embryonal cells in which growth and/or differentiation have become dysregulated during development (summary by Mahamdallie et al., 2015). For a general phenotypic description and discussion of genetic heterogeneity of Wilms tumor, see WT1 (194070). [from OMIM]

Available tests

11 tests are in the database for this condition.

Check Related conditions for additional relevant tests.

Genes See tests for all associated and related genes

  • Also known as: DFNA27, GINGF5, HGF5, NRSF, WT6, XBR, REST
    Summary: RE1 silencing transcription factor

Clinical features

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Practice guidelines

  • NCCN, 2023
    NCCN Clinical Practice Guidelines in Oncology (NCCN GuidelinesĀ®), Wilms Tumor (Nephroblastoma), 2023

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