ProfileGDS4409 / 231579_s_at
TitleInfantile-onset Pompe response to recombinant human lysosomal acid alpha-glucosidase (rhGAA) treatment: quadriceps
OrganismHomo sapiens


patient 1 patient 2 patient 3 patient 4 patient 5 patient 6 patient 7 patient 8 patient 9 patient 10 patient 11 control 1 control 2 control 3 control 4 control 5 control 6 control 7 infantile-onset Pompe control rhGAA none week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 n/a poor clinical outcome positive clinical outcome poor clinical outcome positive clinical outcome poor clinical outcome n/a GSM947487 GSM947488 GSM947489 GSM947490 GSM947491 GSM947492 GSM947493 GSM947494 GSM947495 GSM947496 GSM947497 GSM947498 GSM947499 GSM947500 GSM947501 GSM947502 GSM947503 GSM947504 GSM947505 GSM947506 GSM947507 GSM947508 GSM947509 GSM947510 GSM947511 GSM947512 GSM947513 GSM947514 GSM947515 GSM947516 GSM947517 GSM947518 GSM947480 GSM947481 GSM947482 GSM947483 GSM947484 GSM947485 GSM947486 98% 98% 98% 99% 98% 98% 98% 98% 97% 98% 98% 97% 98% 98% 98% 99% 98% 99% 98% 98% 99% 98% 98% 99% 99% 98% 99% 98% 99% 99% 98% 98% 98% 97% 97% 98% 97% 98% 98% sort by individual sort by disease state sort by agent sort by time sort by other Gene Expression Profile
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SampleTitleValueRank
GSM947487Quadriceps_Pompe_1_00wks11.66898
GSM947488Quadriceps_Pompe_1_12wks11.441498
GSM947489Quadriceps_Pompe_1_52wks11.640698
GSM947490Quadriceps_Pompe_2_00wks11.95999
GSM947491Quadriceps_Pompe_2_12wks11.404398
GSM947492Quadriceps_Pompe_2_52wks11.470798
GSM947493Quadriceps_Pompe_3_00wks11.337998
GSM947494Quadriceps_Pompe_3_12wks11.367298
GSM947495Quadriceps_Pompe_3_52wks10.722797
GSM947496Quadriceps_Pompe_4_00wks11.837998
GSM947497Quadriceps_Pompe_4_12wks11.615298
GSM947498Quadriceps_Pompe_4_52wks10.306697
GSM947499Quadriceps_Pompe_5_00wks11.16898
GSM947500Quadriceps_Pompe_5_12wks11.802798
GSM947501Quadriceps_Pompe_5_52wks11.474698
GSM947502Quadriceps_Pompe_6_00wks11.972799
GSM947503Quadriceps_Pompe_6_12wks11.789198
GSM947504Quadriceps_Pompe_6_52wks12.863399
GSM947505Quadriceps_Pompe_7_00wks11.804798
GSM947506Quadriceps_Pompe_7_12wks11.636798
GSM947507Quadriceps_Pompe_7_52wks12.507899
GSM947508Quadriceps_Pompe_8_00wks11.904398
GSM947509Quadriceps_Pompe_8_12wks11.20798
GSM947510Quadriceps_Pompe_8_52wks12.253999
GSM947511Quadriceps_Pompe_9_00wks12.013799
GSM947512Quadriceps_Pompe_9_12wks11.503998
GSM947513Quadriceps_Pompe_9_52wks12.37599
GSM947514Quadriceps_Pompe_10_00wks11.308698
GSM947515Quadriceps_Pompe_10_12wks12.283299
GSM947516Quadriceps_Pompe_10_52wks12.718899
GSM947517Quadriceps_Pompe_11_00wks11.687598
GSM947518Quadriceps_Pompe_11_12wks11.462998
GSM947480Quadriceps_Control_111.837998
GSM947481Quadriceps_Control_210.945397
GSM947482Quadriceps_Control_31197
GSM947483Quadriceps_Control_411.724698
GSM947484Quadriceps_Control_510.824297
GSM947485Quadriceps_Control_611.384898
GSM947486Quadriceps_Control_711.785298