ProfileGDS4409 / 215696_s_at
TitleInfantile-onset Pompe response to recombinant human lysosomal acid alpha-glucosidase (rhGAA) treatment: quadriceps
OrganismHomo sapiens


patient 1 patient 2 patient 3 patient 4 patient 5 patient 6 patient 7 patient 8 patient 9 patient 10 patient 11 control 1 control 2 control 3 control 4 control 5 control 6 control 7 infantile-onset Pompe control rhGAA none week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 n/a poor clinical outcome positive clinical outcome poor clinical outcome positive clinical outcome poor clinical outcome n/a GSM947487 GSM947488 GSM947489 GSM947490 GSM947491 GSM947492 GSM947493 GSM947494 GSM947495 GSM947496 GSM947497 GSM947498 GSM947499 GSM947500 GSM947501 GSM947502 GSM947503 GSM947504 GSM947505 GSM947506 GSM947507 GSM947508 GSM947509 GSM947510 GSM947511 GSM947512 GSM947513 GSM947514 GSM947515 GSM947516 GSM947517 GSM947518 GSM947480 GSM947481 GSM947482 GSM947483 GSM947484 GSM947485 GSM947486 86% 85% 88% 85% 83% 86% 86% 83% 85% 86% 86% 80% 85% 84% 85% 86% 87% 86% 83% 85% 77% 86% 84% 83% 86% 86% 86% 85% 73% 81% 83% 88% 85% 87% 88% 85% 86% 86% 87% sort by individual sort by disease state sort by agent sort by time sort by other Gene Expression Profile
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SampleTitleValueRank
GSM947487Quadriceps_Pompe_1_00wks7.9892686
GSM947488Quadriceps_Pompe_1_12wks7.8427785
GSM947489Quadriceps_Pompe_1_52wks8.216888
GSM947490Quadriceps_Pompe_2_00wks7.8330185
GSM947491Quadriceps_Pompe_2_12wks7.4902383
GSM947492Quadriceps_Pompe_2_52wks7.966886
GSM947493Quadriceps_Pompe_3_00wks7.9238386
GSM947494Quadriceps_Pompe_3_12wks7.4355583
GSM947495Quadriceps_Pompe_3_52wks7.6923885
GSM947496Quadriceps_Pompe_4_00wks7.9189486
GSM947497Quadriceps_Pompe_4_12wks7.9140686
GSM947498Quadriceps_Pompe_4_52wks6.9257880
GSM947499Quadriceps_Pompe_5_00wks7.8105585
GSM947500Quadriceps_Pompe_5_12wks7.608484
GSM947501Quadriceps_Pompe_5_52wks7.6992285
GSM947502Quadriceps_Pompe_6_00wks7.9433686
GSM947503Quadriceps_Pompe_6_12wks8.12587
GSM947504Quadriceps_Pompe_6_52wks8.0585986
GSM947505Quadriceps_Pompe_7_00wks7.5302783
GSM947506Quadriceps_Pompe_7_12wks7.7265685
GSM947507Quadriceps_Pompe_7_52wks6.5556677
GSM947508Quadriceps_Pompe_8_00wks7.9423886
GSM947509Quadriceps_Pompe_8_12wks7.7324284
GSM947510Quadriceps_Pompe_8_52wks7.4316483
GSM947511Quadriceps_Pompe_9_00wks7.9638786
GSM947512Quadriceps_Pompe_9_12wks7.920986
GSM947513Quadriceps_Pompe_9_52wks8.1074286
GSM947514Quadriceps_Pompe_10_00wks7.7587985
GSM947515Quadriceps_Pompe_10_12wks5.9052773
GSM947516Quadriceps_Pompe_10_52wks7.1855581
GSM947517Quadriceps_Pompe_11_00wks7.4052783
GSM947518Quadriceps_Pompe_11_12wks8.2753988
GSM947480Quadriceps_Control_17.6972785
GSM947481Quadriceps_Control_28.0878987
GSM947482Quadriceps_Control_38.408288
GSM947483Quadriceps_Control_47.641685
GSM947484Quadriceps_Control_57.858486
GSM947485Quadriceps_Control_67.9931686
GSM947486Quadriceps_Control_78.1445387