ProfileGDS4409 / 212694_s_at
TitleInfantile-onset Pompe response to recombinant human lysosomal acid alpha-glucosidase (rhGAA) treatment: quadriceps
OrganismHomo sapiens


patient 1 patient 2 patient 3 patient 4 patient 5 patient 6 patient 7 patient 8 patient 9 patient 10 patient 11 control 1 control 2 control 3 control 4 control 5 control 6 control 7 infantile-onset Pompe control rhGAA none week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 n/a poor clinical outcome positive clinical outcome poor clinical outcome positive clinical outcome poor clinical outcome n/a GSM947487 GSM947488 GSM947489 GSM947490 GSM947491 GSM947492 GSM947493 GSM947494 GSM947495 GSM947496 GSM947497 GSM947498 GSM947499 GSM947500 GSM947501 GSM947502 GSM947503 GSM947504 GSM947505 GSM947506 GSM947507 GSM947508 GSM947509 GSM947510 GSM947511 GSM947512 GSM947513 GSM947514 GSM947515 GSM947516 GSM947517 GSM947518 GSM947480 GSM947481 GSM947482 GSM947483 GSM947484 GSM947485 GSM947486 93% 95% 93% 93% 91% 94% 94% 95% 92% 93% 95% 81% 93% 93% 94% 93% 92% 91% 94% 93% 92% 91% 92% 93% 92% 93% 92% 94% 88% 90% 86% 95% 91% 90% 94% 90% 80% 94% 89% sort by individual sort by disease state sort by agent sort by time sort by other Gene Expression Profile
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SampleTitleValueRank
GSM947487Quadriceps_Pompe_1_00wks9.4472793
GSM947488Quadriceps_Pompe_1_12wks9.9140695
GSM947489Quadriceps_Pompe_1_52wks9.4199293
GSM947490Quadriceps_Pompe_2_00wks9.4414193
GSM947491Quadriceps_Pompe_2_12wks8.8632891
GSM947492Quadriceps_Pompe_2_52wks9.8808694
GSM947493Quadriceps_Pompe_3_00wks9.8183694
GSM947494Quadriceps_Pompe_3_12wks10.072395
GSM947495Quadriceps_Pompe_3_52wks9.1230592
GSM947496Quadriceps_Pompe_4_00wks9.4238393
GSM947497Quadriceps_Pompe_4_12wks9.8769595
GSM947498Quadriceps_Pompe_4_52wks6.9472781
GSM947499Quadriceps_Pompe_5_00wks9.4355593
GSM947500Quadriceps_Pompe_5_12wks9.3828193
GSM947501Quadriceps_Pompe_5_52wks9.5468894
GSM947502Quadriceps_Pompe_6_00wks9.2714893
GSM947503Quadriceps_Pompe_6_12wks9.1679792
GSM947504Quadriceps_Pompe_6_52wks8.9746191
GSM947505Quadriceps_Pompe_7_00wks9.6699294
GSM947506Quadriceps_Pompe_7_12wks9.3632893
GSM947507Quadriceps_Pompe_7_52wks9.0976692
GSM947508Quadriceps_Pompe_8_00wks8.8867291
GSM947509Quadriceps_Pompe_8_12wks9.0781292
GSM947510Quadriceps_Pompe_8_52wks9.2558693
GSM947511Quadriceps_Pompe_9_00wks9.0664192
GSM947512Quadriceps_Pompe_9_12wks9.3691493
GSM947513Quadriceps_Pompe_9_52wks9.2011792
GSM947514Quadriceps_Pompe_10_00wks9.658294
GSM947515Quadriceps_Pompe_10_12wks8.1074288
GSM947516Quadriceps_Pompe_10_52wks8.6738390
GSM947517Quadriceps_Pompe_11_00wks7.8544986
GSM947518Quadriceps_Pompe_11_12wks10.109495
GSM947480Quadriceps_Control_18.8671991
GSM947481Quadriceps_Control_28.7597790
GSM947482Quadriceps_Control_39.779394
GSM947483Quadriceps_Control_48.6503990
GSM947484Quadriceps_Control_56.9101680
GSM947485Quadriceps_Control_69.7265694
GSM947486Quadriceps_Control_78.5449289