ProfileGDS4409 / 205028_at
TitleInfantile-onset Pompe response to recombinant human lysosomal acid alpha-glucosidase (rhGAA) treatment: quadriceps
OrganismHomo sapiens


patient 1 patient 2 patient 3 patient 4 patient 5 patient 6 patient 7 patient 8 patient 9 patient 10 patient 11 control 1 control 2 control 3 control 4 control 5 control 6 control 7 infantile-onset Pompe control rhGAA none week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 n/a poor clinical outcome positive clinical outcome poor clinical outcome positive clinical outcome poor clinical outcome n/a GSM947487 GSM947488 GSM947489 GSM947490 GSM947491 GSM947492 GSM947493 GSM947494 GSM947495 GSM947496 GSM947497 GSM947498 GSM947499 GSM947500 GSM947501 GSM947502 GSM947503 GSM947504 GSM947505 GSM947506 GSM947507 GSM947508 GSM947509 GSM947510 GSM947511 GSM947512 GSM947513 GSM947514 GSM947515 GSM947516 GSM947517 GSM947518 GSM947480 GSM947481 GSM947482 GSM947483 GSM947484 GSM947485 GSM947486 62% 57% 54% 58% 62% 69% 57% 58% 58% 28% 55% 57% 58% 65% 72% 58% 61% 66% 58% 58% 58% 58% 58% 64% 58% 68% 65% 58% 59% 58% 63% 62% 73% 71% 78% 69% 60% 68% 68% sort by individual sort by disease state sort by agent sort by time sort by other Gene Expression Profile
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SampleTitleValueRank
GSM947487Quadriceps_Pompe_1_00wks4.5703162
GSM947488Quadriceps_Pompe_1_12wks3.7929757
GSM947489Quadriceps_Pompe_1_52wks3.4228554
GSM947490Quadriceps_Pompe_2_00wks3.8813558
GSM947491Quadriceps_Pompe_2_12wks4.5478562
GSM947492Quadriceps_Pompe_2_52wks5.5195369
GSM947493Quadriceps_Pompe_3_00wks3.829157
GSM947494Quadriceps_Pompe_3_12wks3.9155358
GSM947495Quadriceps_Pompe_3_52wks3.9589858
GSM947496Quadriceps_Pompe_4_00wks2.358428
GSM947497Quadriceps_Pompe_4_12wks3.5019555
GSM947498Quadriceps_Pompe_4_52wks3.9101657
GSM947499Quadriceps_Pompe_5_00wks3.8828158
GSM947500Quadriceps_Pompe_5_12wks5.0205165
GSM947501Quadriceps_Pompe_5_52wks5.9091872
GSM947502Quadriceps_Pompe_6_00wks3.8764758
GSM947503Quadriceps_Pompe_6_12wks4.4316461
GSM947504Quadriceps_Pompe_6_52wks5.1933666
GSM947505Quadriceps_Pompe_7_00wks3.8632858
GSM947506Quadriceps_Pompe_7_12wks3.8745158
GSM947507Quadriceps_Pompe_7_52wks3.9262758
GSM947508Quadriceps_Pompe_8_00wks3.8818458
GSM947509Quadriceps_Pompe_8_12wks3.8764758
GSM947510Quadriceps_Pompe_8_52wks4.7617264
GSM947511Quadriceps_Pompe_9_00wks4.0322358
GSM947512Quadriceps_Pompe_9_12wks5.4218868
GSM947513Quadriceps_Pompe_9_52wks4.8427765
GSM947514Quadriceps_Pompe_10_00wks3.8535258
GSM947515Quadriceps_Pompe_10_12wks3.9770559
GSM947516Quadriceps_Pompe_10_52wks3.8769558
GSM947517Quadriceps_Pompe_11_00wks4.6796963
GSM947518Quadriceps_Pompe_11_12wks4.470762
GSM947480Quadriceps_Control_16.0371173
GSM947481Quadriceps_Control_25.766671
GSM947482Quadriceps_Control_36.7431678
GSM947483Quadriceps_Control_45.4716869
GSM947484Quadriceps_Control_54.1650460
GSM947485Quadriceps_Control_65.2714868
GSM947486Quadriceps_Control_75.3662168