ProfileGDS4409 / 201324_at
TitleInfantile-onset Pompe response to recombinant human lysosomal acid alpha-glucosidase (rhGAA) treatment: quadriceps
OrganismHomo sapiens


patient 1 patient 2 patient 3 patient 4 patient 5 patient 6 patient 7 patient 8 patient 9 patient 10 patient 11 control 1 control 2 control 3 control 4 control 5 control 6 control 7 infantile-onset Pompe control rhGAA none week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 n/a poor clinical outcome positive clinical outcome poor clinical outcome positive clinical outcome poor clinical outcome n/a GSM947487 GSM947488 GSM947489 GSM947490 GSM947491 GSM947492 GSM947493 GSM947494 GSM947495 GSM947496 GSM947497 GSM947498 GSM947499 GSM947500 GSM947501 GSM947502 GSM947503 GSM947504 GSM947505 GSM947506 GSM947507 GSM947508 GSM947509 GSM947510 GSM947511 GSM947512 GSM947513 GSM947514 GSM947515 GSM947516 GSM947517 GSM947518 GSM947480 GSM947481 GSM947482 GSM947483 GSM947484 GSM947485 GSM947486 93% 91% 93% 95% 93% 92% 91% 94% 90% 94% 95% 88% 89% 95% 95% 93% 93% 97% 95% 95% 97% 94% 94% 96% 95% 93% 95% 91% 97% 98% 97% 92% 96% 90% 92% 94% 91% 93% 95% sort by individual sort by disease state sort by agent sort by time sort by other Gene Expression Profile
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SampleTitleValueRank
GSM947487Quadriceps_Pompe_1_00wks9.5039193
GSM947488Quadriceps_Pompe_1_12wks8.8437591
GSM947489Quadriceps_Pompe_1_52wks9.283293
GSM947490Quadriceps_Pompe_2_00wks9.9921995
GSM947491Quadriceps_Pompe_2_12wks9.2871193
GSM947492Quadriceps_Pompe_2_52wks9.1074292
GSM947493Quadriceps_Pompe_3_00wks8.9160291
GSM947494Quadriceps_Pompe_3_12wks9.5898494
GSM947495Quadriceps_Pompe_3_52wks8.6503990
GSM947496Quadriceps_Pompe_4_00wks9.6621194
GSM947497Quadriceps_Pompe_4_12wks10.064595
GSM947498Quadriceps_Pompe_4_52wks8.0878988
GSM947499Quadriceps_Pompe_5_00wks8.5761789
GSM947500Quadriceps_Pompe_5_12wks9.904395
GSM947501Quadriceps_Pompe_5_52wks9.8378995
GSM947502Quadriceps_Pompe_6_00wks9.3906293
GSM947503Quadriceps_Pompe_6_12wks9.4785293
GSM947504Quadriceps_Pompe_6_52wks10.830197
GSM947505Quadriceps_Pompe_7_00wks9.8789195
GSM947506Quadriceps_Pompe_7_12wks9.8554795
GSM947507Quadriceps_Pompe_7_52wks11.007897
GSM947508Quadriceps_Pompe_8_00wks9.8261794
GSM947509Quadriceps_Pompe_8_12wks9.5800894
GSM947510Quadriceps_Pompe_8_52wks10.429796
GSM947511Quadriceps_Pompe_9_00wks10.158295
GSM947512Quadriceps_Pompe_9_12wks9.4023493
GSM947513Quadriceps_Pompe_9_52wks10.228595
GSM947514Quadriceps_Pompe_10_00wks9.0078191
GSM947515Quadriceps_Pompe_10_12wks10.800897
GSM947516Quadriceps_Pompe_10_52wks11.187598
GSM947517Quadriceps_Pompe_11_00wks10.464897
GSM947518Quadriceps_Pompe_11_12wks9.2968892
GSM947480Quadriceps_Control_110.337996
GSM947481Quadriceps_Control_28.7597790
GSM947482Quadriceps_Control_39.1933692
GSM947483Quadriceps_Control_49.5585994
GSM947484Quadriceps_Control_58.7949291
GSM947485Quadriceps_Control_69.2558693
GSM947486Quadriceps_Control_710.052795