ProfileGDS4409 / 1561503_at
TitleInfantile-onset Pompe response to recombinant human lysosomal acid alpha-glucosidase (rhGAA) treatment: quadriceps
OrganismHomo sapiens


patient 1 patient 2 patient 3 patient 4 patient 5 patient 6 patient 7 patient 8 patient 9 patient 10 patient 11 control 1 control 2 control 3 control 4 control 5 control 6 control 7 infantile-onset Pompe control rhGAA none week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 n/a poor clinical outcome positive clinical outcome poor clinical outcome positive clinical outcome poor clinical outcome n/a GSM947487 GSM947488 GSM947489 GSM947490 GSM947491 GSM947492 GSM947493 GSM947494 GSM947495 GSM947496 GSM947497 GSM947498 GSM947499 GSM947500 GSM947501 GSM947502 GSM947503 GSM947504 GSM947505 GSM947506 GSM947507 GSM947508 GSM947509 GSM947510 GSM947511 GSM947512 GSM947513 GSM947514 GSM947515 GSM947516 GSM947517 GSM947518 GSM947480 GSM947481 GSM947482 GSM947483 GSM947484 GSM947485 GSM947486 22% 32% 22% 37% 49% 37% 22% 41% 34% 27% 34% 32% 35% 57% 64% 23% 56% 76% 35% 22% 37% 36% 33% 26% 35% 63% 48% 37% 39% 37% 32% 52% 42% 76% 84% 62% 52% 43% 73% sort by individual sort by disease state sort by agent sort by time sort by other Gene Expression Profile
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SampleTitleValueRank
GSM947487Quadriceps_Pompe_1_00wks2.312522
GSM947488Quadriceps_Pompe_1_12wks2.3974632
GSM947489Quadriceps_Pompe_1_52wks2.3159222
GSM947490Quadriceps_Pompe_2_00wks2.4550837
GSM947491Quadriceps_Pompe_2_12wks2.9091849
GSM947492Quadriceps_Pompe_2_52wks2.4672837
GSM947493Quadriceps_Pompe_3_00wks2.3134822
GSM947494Quadriceps_Pompe_3_12wks2.5341841
GSM947495Quadriceps_Pompe_3_52wks2.4663134
GSM947496Quadriceps_Pompe_4_00wks2.3461927
GSM947497Quadriceps_Pompe_4_12wks2.437534
GSM947498Quadriceps_Pompe_4_52wks2.4384832
GSM947499Quadriceps_Pompe_5_00wks2.4487335
GSM947500Quadriceps_Pompe_5_12wks3.8154357
GSM947501Quadriceps_Pompe_5_52wks4.7197364
GSM947502Quadriceps_Pompe_6_00wks2.3110323
GSM947503Quadriceps_Pompe_6_12wks3.6743256
GSM947504Quadriceps_Pompe_6_52wks6.5703176
GSM947505Quadriceps_Pompe_7_00wks2.437535
GSM947506Quadriceps_Pompe_7_12wks2.3134822
GSM947507Quadriceps_Pompe_7_52wks2.5092837
GSM947508Quadriceps_Pompe_8_00wks2.4521536
GSM947509Quadriceps_Pompe_8_12wks2.4121133
GSM947510Quadriceps_Pompe_8_52wks2.3740226
GSM947511Quadriceps_Pompe_9_00wks2.4384835
GSM947512Quadriceps_Pompe_9_12wks4.6933663
GSM947513Quadriceps_Pompe_9_52wks2.8017648
GSM947514Quadriceps_Pompe_10_00wks2.4609437
GSM947515Quadriceps_Pompe_10_12wks2.6191439
GSM947516Quadriceps_Pompe_10_52wks2.4716837
GSM947517Quadriceps_Pompe_11_00wks2.4389732
GSM947518Quadriceps_Pompe_11_12wks3.1196352
GSM947480Quadriceps_Control_12.5996142
GSM947481Quadriceps_Control_26.4560676
GSM947482Quadriceps_Control_37.716884
GSM947483Quadriceps_Control_44.4306662
GSM947484Quadriceps_Control_53.2460952
GSM947485Quadriceps_Control_62.6127943
GSM947486Quadriceps_Control_76.108473