ProfileGDS4409 / 1558411_at
TitleInfantile-onset Pompe response to recombinant human lysosomal acid alpha-glucosidase (rhGAA) treatment: quadriceps
OrganismHomo sapiens


patient 1 patient 2 patient 3 patient 4 patient 5 patient 6 patient 7 patient 8 patient 9 patient 10 patient 11 control 1 control 2 control 3 control 4 control 5 control 6 control 7 infantile-onset Pompe control rhGAA none week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 n/a poor clinical outcome positive clinical outcome poor clinical outcome positive clinical outcome poor clinical outcome n/a GSM947487 GSM947488 GSM947489 GSM947490 GSM947491 GSM947492 GSM947493 GSM947494 GSM947495 GSM947496 GSM947497 GSM947498 GSM947499 GSM947500 GSM947501 GSM947502 GSM947503 GSM947504 GSM947505 GSM947506 GSM947507 GSM947508 GSM947509 GSM947510 GSM947511 GSM947512 GSM947513 GSM947514 GSM947515 GSM947516 GSM947517 GSM947518 GSM947480 GSM947481 GSM947482 GSM947483 GSM947484 GSM947485 GSM947486 28% 28% 28% 28% 30% 28% 28% 27% 31% 28% 28% 29% 28% 28% 29% 28% 28% 27% 28% 28% 29% 29% 29% 33% 28% 28% 29% 28% 30% 28% 32% 28% 26% 28% 28% 27% 28% 27% 28% sort by individual sort by disease state sort by agent sort by time sort by other Gene Expression Profile
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SampleTitleValueRank
GSM947487Quadriceps_Pompe_1_00wks2.3588928
GSM947488Quadriceps_Pompe_1_12wks2.3608428
GSM947489Quadriceps_Pompe_1_52wks2.3764728
GSM947490Quadriceps_Pompe_2_00wks2.3613328
GSM947491Quadriceps_Pompe_2_12wks2.391630
GSM947492Quadriceps_Pompe_2_52wks2.3627928
GSM947493Quadriceps_Pompe_3_00wks2.3632828
GSM947494Quadriceps_Pompe_3_12wks2.3535227
GSM947495Quadriceps_Pompe_3_52wks2.4355531
GSM947496Quadriceps_Pompe_4_00wks2.3564528
GSM947497Quadriceps_Pompe_4_12wks2.3803728
GSM947498Quadriceps_Pompe_4_52wks2.4091829
GSM947499Quadriceps_Pompe_5_00wks2.370628
GSM947500Quadriceps_Pompe_5_12wks2.362328
GSM947501Quadriceps_Pompe_5_52wks2.387729
GSM947502Quadriceps_Pompe_6_00wks2.3544928
GSM947503Quadriceps_Pompe_6_12wks2.3647528
GSM947504Quadriceps_Pompe_6_52wks2.3491227
GSM947505Quadriceps_Pompe_7_00wks2.3657228
GSM947506Quadriceps_Pompe_7_12wks2.3681628
GSM947507Quadriceps_Pompe_7_52wks2.4003929
GSM947508Quadriceps_Pompe_8_00wks2.37529
GSM947509Quadriceps_Pompe_8_12wks2.3701229
GSM947510Quadriceps_Pompe_8_52wks2.4506833
GSM947511Quadriceps_Pompe_9_00wks2.3608428
GSM947512Quadriceps_Pompe_9_12wks2.3647528
GSM947513Quadriceps_Pompe_9_52wks2.3857429
GSM947514Quadriceps_Pompe_10_00wks2.3554728
GSM947515Quadriceps_Pompe_10_12wks2.4516630
GSM947516Quadriceps_Pompe_10_52wks2.3701228
GSM947517Quadriceps_Pompe_11_00wks2.437532
GSM947518Quadriceps_Pompe_11_12wks2.3593828
GSM947480Quadriceps_Control_12.3569326
GSM947481Quadriceps_Control_22.3696328
GSM947482Quadriceps_Control_32.3642628
GSM947483Quadriceps_Control_42.3652327
GSM947484Quadriceps_Control_52.3891628
GSM947485Quadriceps_Control_62.3647527
GSM947486Quadriceps_Control_72.3588928