ProfileGDS4409 / 1552266_at
TitleInfantile-onset Pompe response to recombinant human lysosomal acid alpha-glucosidase (rhGAA) treatment: quadriceps
OrganismHomo sapiens


patient 1 patient 2 patient 3 patient 4 patient 5 patient 6 patient 7 patient 8 patient 9 patient 10 patient 11 control 1 control 2 control 3 control 4 control 5 control 6 control 7 infantile-onset Pompe control rhGAA none week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 week 52 week 0 week 12 n/a poor clinical outcome positive clinical outcome poor clinical outcome positive clinical outcome poor clinical outcome n/a GSM947487 GSM947488 GSM947489 GSM947490 GSM947491 GSM947492 GSM947493 GSM947494 GSM947495 GSM947496 GSM947497 GSM947498 GSM947499 GSM947500 GSM947501 GSM947502 GSM947503 GSM947504 GSM947505 GSM947506 GSM947507 GSM947508 GSM947509 GSM947510 GSM947511 GSM947512 GSM947513 GSM947514 GSM947515 GSM947516 GSM947517 GSM947518 GSM947480 GSM947481 GSM947482 GSM947483 GSM947484 GSM947485 GSM947486 35% 58% 56% 36% 34% 33% 48% 36% 55% 49% 37% 67% 42% 34% 34% 33% 34% 51% 35% 34% 34% 35% 36% 64% 57% 33% 41% 35% 34% 33% 45% 33% 32% 34% 33% 32% 34% 33% 32% sort by individual sort by disease state sort by agent sort by time sort by other Gene Expression Profile
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SampleTitleValueRank
GSM947487Quadriceps_Pompe_1_00wks2.433135
GSM947488Quadriceps_Pompe_1_12wks3.8974658
GSM947489Quadriceps_Pompe_1_52wks3.7426856
GSM947490Quadriceps_Pompe_2_00wks2.4438536
GSM947491Quadriceps_Pompe_2_12wks2.4438534
GSM947492Quadriceps_Pompe_2_52wks2.4189533
GSM947493Quadriceps_Pompe_3_00wks2.7797848
GSM947494Quadriceps_Pompe_3_12wks2.441936
GSM947495Quadriceps_Pompe_3_52wks3.5786155
GSM947496Quadriceps_Pompe_4_00wks2.9018549
GSM947497Quadriceps_Pompe_4_12wks2.4814537
GSM947498Quadriceps_Pompe_4_52wks5.1386767
GSM947499Quadriceps_Pompe_5_00wks2.5756842
GSM947500Quadriceps_Pompe_5_12wks2.4321334
GSM947501Quadriceps_Pompe_5_52wks2.437534
GSM947502Quadriceps_Pompe_6_00wks2.4033233
GSM947503Quadriceps_Pompe_6_12wks2.4316434
GSM947504Quadriceps_Pompe_6_52wks3.1220751
GSM947505Quadriceps_Pompe_7_00wks2.4433635
GSM947506Quadriceps_Pompe_7_12wks2.4321334
GSM947507Quadriceps_Pompe_7_52wks2.4555734
GSM947508Quadriceps_Pompe_8_00wks2.4467835
GSM947509Quadriceps_Pompe_8_12wks2.4570336
GSM947510Quadriceps_Pompe_8_52wks4.7324264
GSM947511Quadriceps_Pompe_9_00wks3.8344757
GSM947512Quadriceps_Pompe_9_12wks2.4174833
GSM947513Quadriceps_Pompe_9_52wks2.5537141
GSM947514Quadriceps_Pompe_10_00wks2.4360335
GSM947515Quadriceps_Pompe_10_12wks2.5146534
GSM947516Quadriceps_Pompe_10_52wks2.4204133
GSM947517Quadriceps_Pompe_11_00wks2.7241245
GSM947518Quadriceps_Pompe_11_12wks2.408233
GSM947480Quadriceps_Control_12.4106532
GSM947481Quadriceps_Control_22.429234
GSM947482Quadriceps_Control_32.4228533
GSM947483Quadriceps_Control_42.4174832
GSM947484Quadriceps_Control_52.4560534
GSM947485Quadriceps_Control_62.4233433
GSM947486Quadriceps_Control_72.4033232