Figure 3.

Figure 3.

Muscle MRI (coronal images of the thighs and calves; T1-weighted sequence)

A. Diffuse bright appearance of the anterior compartment of the thighs (upper images), particularly in the vastus lateralis muscles, and the posterior compartment of the calves (lower images) in an individual age seven years

B. Relative sparing of the posterior compartment of the thighs (upper images) in an individual age 30 years with severe disease

C. Specific involvement of the vastus lateralis muscles (white asterisks) with sparing of other thigh muscles in an individual age 38 years

From Mercier et al [2015]

From: Hereditary Fibrosing Poikiloderma with Tendon Contractures, Myopathy, and Pulmonary Fibrosis

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