Table 1. 2020 World Health Organization Classification of Vascular Tumorsa

Category Vascular Tumor Type
Benign Hemangioma NOS
Intramuscular hemangioma
Arteriovenous hemangioma
Venous hemangioma
Epithelioid hemangioma
Lymphangioma NOS
Cystic lymphangioma
Acquired tufted hemangioma
Intermediate (locally aggressive) Kaposiform hemangioendothelioma
Intermediate (rarely metastasizing) Retiform hemangioendothelioma
Papillary intralymphatic angioendothelioma
Composite hemangioendothelioma
Kaposi sarcoma
Pseudomyogenic (epithelioid sarcoma–like) hemangioendothelioma
Malignant Epithelioid hemangioendothelioma NOS
Angiosarcoma

NOS = not otherwise specified.

aAdapted from the WHO Classification of Tumours Editorial Board.[3]

From: Childhood Vascular Tumors Treatment (PDQ®)

Cover of PDQ Cancer Information Summaries
PDQ Cancer Information Summaries [Internet].
Bethesda (MD): National Cancer Institute (US); 2002-.

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