Figure 2. . Metabolism of glycine by glycine cleavage enzyme.

Figure 2.

Metabolism of glycine by glycine cleavage enzyme. Glycine enters the four-protein enzyme complex at the lower left, where it is decarboxylated by the P-protein (also known as glycine decarboxylase). A defect of the P-, H-, or T-proteins of this complex causes glycine encephalopathy.

From: Nonketotic Hyperglycinemia

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